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anti-UQCRQ antibody :: Rabbit ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa Polyclonal Antibody

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Catalog # MBS710103
Unit / Price
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  0.05 mL  /  $230 +1 FREE 8GB USB
  0.15 mL  /  $500 +1 FREE 8GB USB
anti-UQCRQ antibody
Product Name

ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa (UQCRQ), Polyclonal Antibody

Popular Item
Full Product Name

Rabbit anti-human ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa polyclonal Antibody

Product Synonym Names
ubiquinol-cytochrome c reductase; complex III subunit VII; 9.5kDa; UQCRQ; QCR8; QP-C; QPC
Research Use Only
For Research Use Only. Not for use in diagnostic procedures.
OMIM
gene 615159
Clonality
Polyclonal
Isotype
IgG
Host
Rabbit
Species Reactivity
Human, Mouse, Rat
Purity/Purification
Antigen Affinity Purified
Immunogen
Human UQCRQ
Storage Buffer
PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20 degree C, Avoid freeze / thaw cycles.
Santa Cruz Alternative
Potential replacement for Santa Cruz Biotechnology antibody catalog# sc-74880
ISO Certification
Manufactured in an ISO 9001:2008 Certified Laboratory.
Other Notes
Small volumes of anti-UQCRQ antibody vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
Applications Tested/Suitable for anti-UQCRQ antibody
ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC)
NCBI/Uniprot data below describe general gene information for UQCRQ. It may not necessarily be applicable to this product.
NCBI GI #
NCBI GeneID
NCBI Accession #
UniProt Secondary Accession #
UniProt Related Accession #
Molecular Weight
NCBI Official Full Name
Ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
NCBI Official Synonym Full Names
ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa
NCBI Official Symbol
UQCRQ  [Similar Products]
NCBI Official Synonym Symbols
QPC; QCR8; QP-C; UQCR7; MC3DN4
  [Similar Products]
NCBI Protein Information
cytochrome b-c1 complex subunit 8; complex III subunit 8; complex III subunit VIII; low molecular mass ubiquinone-binding protein (9.5kD); ubiquinol-cytochrome c reductase complex 9.5 kDa protein; ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C
UniProt Protein Name
Cytochrome b-c1 complex subunit 8
UniProt Synonym Protein Names
Complex III subunit 8; Complex III subunit VIII; Ubiquinol-cytochrome c reductase complex 9.5 kDa protein; Ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C
UniProt Gene Name
UQCRQ  [Similar Products]
UniProt Entry Name
QCR8_HUMAN
NCBI Summary for UQCRQ
This gene encodes a ubiquinone-binding protein of low molecular mass. This protein is a small core-associated protein and a subunit of ubiquinol-cytochrome c reductase complex III, which is part of the mitochondrial respiratory chain. [provided by RefSeq, Jul 2008]
UniProt Comments for UQCRQ
UQCRQ: This is a component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain. This subunit, together with cytochrome b, binds to ubiquinone. Defects in UQCRQ are a cause of mitochondrial complex III deficiency (MT-C3D). A disorder of the mitochondrial respiratory chain resulting in a highly variable phenotype depending on which tissues are affected. Clinical features include mitochondrial encephalopathy, psychomotor retardation, ataxia, severe failure to thrive, liver dysfunction, renal tubulopathy, muscle weakness and exercise intolerance. Belongs to the UQCRQ/QCR8 family.

Protein type: Oxidoreductase; Mitochondrial; Energy Metabolism - oxidative phosphorylation

Chromosomal Location of Human Ortholog: 5q31.1

Cellular Component: mitochondrion; mitochondrial inner membrane

Molecular Function: ubiquinol-cytochrome-c reductase activity

Biological Process: cellular metabolic process; hypothalamus development; pons development; hippocampus development; midbrain development; cerebellar Purkinje cell layer development; subthalamus development; pyramidal neuron development; thalamus development

Disease: Mitochondrial Complex Iii Deficiency, Nuclear Type 4
Precautions
All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
Disclaimer
While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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