View our list of available Coronavirus (COVID-19, SARS-CoV-2, 2019-nCOV) antibodies, recombinant proteins, ELISA Kits... Options Full Datasheet Printer Friendly Datasheet Prepare for Printing Full Datasheet Printer Friendly Datasheet Prepare for Printing Have Questions? Ask Us! Request A Quote Today! Add To Compare List SGSH antibody pair kit :: Human N-Sulfoglucosamine Sulfohydrolase (SGSH) Antibody Pair Kit Catalog # MBS2103783 (SPECIAL PROMOTION: Get FREE $5 Starbucks gift card (Maximum 5 gift cards/product). Gift card(s) will be included with shipment) Unit / Price 5x96 Tests / $945 +1 FREE 8GB USB 5x96 Tests + MBS2090685 (Ab Pairs Support Pack 1, 5x96 Tests) / $1,020 +1 FREE 8GB USB 10x96 Tests / $1,490 +1 FREE 8GB USB 10x96 Tests + MBS2090685 (Ab Pairs Support Pack 1, 10x96 Tests) / $1,610 +2 FREE 8GB USB Product Name Product Info Accession #s Product Desc Diseases/Tissues/Pathways Applications References Product Name N-Sulfoglucosamine Sulfohydrolase (SGSH), Antibody Pair Kit Full Product Name Human N-Sulfoglucosamine Sulfohydrolase (SGSH) Antibody Pair Kit (with Standard) Product Synonym Names HSS; MPS3A; SFMD; Sulfamidase; Sulfoglucosamine sulfamidase Product Gene Name SGSH antibody pair kit[Similar Products] Research Use Only For Research Use Only. Not for use in diagnostic procedures. TOP Request for Current Manual Insert Request Current Manual OMIM U30894 mRNA Species Reactivity Human Samples Tissue Homogenates, Cell Lysates and Other Biological Fluids Detection Range 0.312-20ng/mL Standard Recombinant SGSH (Lyophilized, 1 vial-10ug) Capture Antibody Rabbit polyclonal antibody (Liquid, 1 vial-400mug/800muL) Detection Antibody Biotinylated Rabbit polyclonal antibody (Liquid, 1 vial-100mug/500muL) Producte Usage Raw materials can be used for preparation of 5x96T or 10x96T ELISA Kits. Antibody Support Pack Antibody Support Pack (Buffer Pack) is sold separately as catalog #MBS2090685 ISO Certification Manufactured in an ISO 9001:2008 and ISO 13485:2003 Certified Laboratory. Supply Chain Verification Manufactured in a lab with traceable raw materials. Bulk orders can typically be prepared to the customer’s specifications, please inquire. Product Note Select online data sheet information is drawn from bioinformatics databases, occasionally resulting in ambiguous or non-relevant product information. It is the responsibility of the customer to review, verify, and evaluate the information to make sure it matches their requirements before purchasing the kit. Our ELISA Kit assays are dynamic research tools and sometimes they may be updated and improved. If the format of this assay is important to you then please request the current manual or contact our technical support team with a presales inquiry before placing an order. We will confirm the current details of the assay. We cannot guarantee the sample manual posted online is the most current manual, it is intended to serve as an example only. Please refer to the instructions For Use provided with the assay kit for precise details. Other Notes Small volumes of SGSH antibody pair kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply. TOP Product Categories/Family for SGSH antibody pair kit Enzyme & Kinase Applications Tested/Suitable for SGSH antibody pair kit ELISA (EIA), Chemiluminescence Immunoassays (CLIA), ELISPOT, Luminex TOP NCBI/Uniprot data below describe general gene information for SGSH. It may not necessarily be applicable to this product. NCBI GI # 28703787 NCBI GeneID 6448 NCBI Accession # AAH47318.1 [Other Products] UniProt Secondary Accession # A8K5E2[Other Products] UniProt Related Accession # P51688[Other Products] Molecular Weight 56,695 Da TOP NCBI Official Full Name N-sulfoglucosamine sulfohydrolase NCBI Official Synonym Full Names N-sulfoglucosamine sulfohydrolase NCBI Official Symbol SGSH [Similar Products] NCBI Official Synonym Symbols HSS; SFMD; MPS3A [Similar Products] NCBI Protein Information N-sulphoglucosamine sulphohydrolase UniProt Protein Name N-sulphoglucosamine sulphohydrolase UniProt Synonym Protein Names Sulfoglucosamine sulfamidase; Sulphamidase Protein Family N-sulphoglucosamine sulphohydrolase UniProt Gene Name SGSH [Similar Products] UniProt Synonym Gene Names HSS [Similar Products] TOP NCBI Summary for SGSH This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017] TOP UniProt Comments for SGSH Catalyzes a step in lysosomal heparan sulfate degradation. Research Articles on SGSH 1. CSF enzyme activity levels for either SGSH (in MPS IIIA subjects) or NAGLU (in MPS IIIB) significantly differed from normal controls. Several other behavioral or functional measures were found to be uninformative in this population, including timed functional motor tests. TOP Precautions All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines. Disclaimer While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information. TOP Products associated with SGSH antibody pair kit Reference Product PubMed Publications NAGLU antibody pair kit >13 publications with SGSH and NAGLU HGSNAT antibody pair kit >7 publications with SGSH and HGSNAT IDUA antibody pair kit >4 publications with SGSH and IDUA SUMF1 antibody pair kit >3 publications with SGSH and SUMF1 CLN6 antibody pair kit >1 publications with SGSH and CLN6 Pathways associated with SGSH antibody pair kit Products by Pathway Pathway Diagram Glycosaminoglycan Degradation Pathway antibodies Glycosaminoglycan Degradation Pathway Diagram Glycosaminoglycan Degradation Pathway antibodies Glycosaminoglycan Degradation Pathway Diagram Glycosaminoglycan Metabolism Pathway antibodies Glycosaminoglycan Metabolism Pathway Diagram HS-GAG Degradation Pathway antibodies HS-GAG Degradation Pathway Diagram Heparan Sulfate Degradation Pathway antibodies Heparan Sulfate Degradation Pathway Diagram Heparan Sulfate Degradation Pathway antibodies Heparan Sulfate Degradation Pathway Diagram Heparan Sulfate/heparin (HS-GAG) Metabolism Pathway antibodies Heparan Sulfate/heparin (HS-GAG) Metabolism Pathway Diagram Lysosome Pathway antibodies Lysosome Pathway Diagram Lysosome Pathway antibodies Lysosome Pathway Diagram Metabolic Pathways antibodies Metabolic Pathways Diagram Diseases associated with SGSH antibody pair kit Disease Name Pubmed Publications Mucopolysaccharidosis III Antibodies >37 publications with SGSH and Mucopolysaccharidosis III Nervous System Diseases Antibodies >10 publications with SGSH and Nervous System Diseases Death Antibodies >8 publications with SGSH and Death Liver Diseases Antibodies >3 publications with SGSH and Liver Diseases Diabetes Mellitus Antibodies >1 publications with SGSH and Diabetes Mellitus Vascular Diseases Antibodies >1 publications with SGSH and Vascular Diseases Atrophy Antibodies >1 publications with SGSH and Atrophy Immune System Diseases Antibodies >1 publications with SGSH and Immune System Diseases Proteinuria Antibodies >1 publications with SGSH and Proteinuria Learning Disorders Antibodies >1 publications with SGSH and Learning Disorders Organs/Tissues associated with SGSH antibody pair kit Organ/Tissue Name Pubmed Publications Brain Antibodies >21 publications with SGSH and Brain Blood Antibodies >13 publications with SGSH and Blood Liver Antibodies >6 publications with SGSH and Liver Bone Antibodies >3 publications with SGSH and Bone Eye Antibodies >1 publications with SGSH and Eye Kidney Antibodies >1 publications with SGSH and Kidney Skin Antibodies >1 publications with SGSH and Skin Spleen Antibodies >1 publications with SGSH and Spleen Vascular Antibodies >1 publications with SGSH and Vascular Lung Antibodies >1 publications with SGSH and Lung TOP © 2006-24 MyBioSource.com. 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