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anti-FKRP antibody :: FKRP Antibody

Scan QR to view Datasheet Catalog #    MBS855737
Western Blot (WB)
Unit / Price
0.1 mg  /  $215 +1 FREE 8GB USB
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

FKRP, Antibody

 Also Known As   

FKRP Antibody

 Product Synonym Names    Fukutin-related protein; EC 2.-.-.-; FKRP
 Product Gene Name   

anti-FKRP antibody

[Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
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 OMIM    606596
 3D Structure    ModBase 3D Structure for Q9H9S5
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 Species Reactivity    Human, Mouse, Rat
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 Specificity    FKRP antibody detects endogenous levels of total FKRP protein.
 Purity/Purification    Affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
 Form/Format    In phosphate buffered saline (without Mg2+ and Ca2+), pH 7.4, 150mM NaCl, 0.02% sodium azide and 50% glycerol.
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 Immunogen    The antiserum was produced against synthesized peptide derived from N-terminal of human FKRP.
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 Preparation and Storage    Store at-20 degree C for 1 year.
 Other Notes    Small volumes of anti-FKRP antibody vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
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 Product Categories/Family for anti-FKRP antibody    Autophagy antibody; Cancer; Cardiovascular; Cell Biology; Epigenetics & Nuclear Signaling; Developmental Biologys; Immunology; Drug Discovery Products; Metabolism; Neuroscience; Signal Transduction; Stem Cells
 Applications Tested/Suitable for anti-FKRP antibody   

Western Blot (WB), ELISA (EIA)

 Application Notes for anti-FKRP antibody    WB: 1:500~1:1000
ELISA: 1:20000
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 Western Blot (WB) of anti-FKRP antibody    Western blot analysis of extracts from Jurkat cells and COLO205 cells, using FKRP antibody.
anti-FKRP antibody Western Blot (WB) (WB) image
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NCBI/Uniprot data below describe general gene information for FKRP. It may not necessarily be applicable to this product.
 NCBI GI #    89941475
 NCBI GeneID    79147
 NCBI Accession #    NP_001034974.1 [Other Products]
 NCBI GenBank Nucleotide #    NM_001039885.2 [Other Products]
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 UniProt Primary Accession #    Q9H9S5 [Other Products]
 UniProt Secondary Accession #    A8K5G7 [Other Products]
 UniProt Related Accession #    Q9H9S5 [Other Products]
 Molecular Weight    54,568 Da
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 NCBI Official Full Name    fukutin-related protein
 NCBI Official Synonym Full Names    fukutin related protein
 NCBI Official Symbol    FKRP [Similar Products]
 NCBI Official Synonym Symbols   
[Similar Products]
 NCBI Protein Information    fukutin-related protein
 UniProt Protein Name    Fukutin-related protein
 Protein Family    Fukutin-related protein
 UniProt Gene Name    FKRP [Similar Products]
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 NCBI Summary for FKRP    This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, cognitive disability, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008]
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 UniProt Comments for FKRP    Transferase involved in the biosynthesis of the phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-3-N-acetylglucosamine-beta-4-(phosphate-6-)mannose), a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity.
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Product References and Citations for anti-FKRP antibody

   Brockington M., Am. J. Hum. Genet. 69:1198-1209(2001). Ota T., Nat. Genet. 36:40-45(2004). Brockington M., Hum. Mol. Genet. 10:2851-2859(2001).
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 Research Articles on FKRP    1. Fukutin, FKRP, and TMEM5 form a complex while maintaining each of their enzyme activities. Data showed that endogenous fukutin and FKRP enzyme activities coexist with TMEM5 enzyme activity, and suggest the possibility that formation of this enzyme complex may contribute to specific and prompt biosynthesis of glycans that are required for dystroglycan function.
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 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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Diseases associated with anti-FKRP antibodyOrgans/Tissues associated with anti-FKRP antibody
 Disease Name  Pubmed Publications
 Walker-Warburg Syndrome Antibodies  >40 publications with FKRP and Walker-Warburg Syndrome
 Heart Diseases Antibodies  >14 publications with FKRP and Heart Diseases
 Cardiovascular Diseases Antibodies  >14 publications with FKRP and Cardiovascular Diseases
 Nervous System Malformations Antibodies  >13 publications with FKRP and Nervous System Malformations
 Hypertrophy Antibodies  >9 publications with FKRP and Hypertrophy
 Atrophy Antibodies  >6 publications with FKRP and Atrophy
 Inflammation Antibodies  >4 publications with FKRP and Inflammation
 Fibrosis Antibodies  >2 publications with FKRP and Fibrosis
 Heart Defects, Congenital Antibodies  >1 publications with FKRP and Heart Defects, Congenital
 Kidney Diseases Antibodies  >1 publications with FKRP and Kidney Diseases
 Organ/Tissue Name  Pubmed Publications
 Muscle Antibodies  >98 publications with FKRP and Muscle
 Brain Antibodies  >60 publications with FKRP and Brain
 Eye Antibodies  >46 publications with FKRP and Eye
 Blood Antibodies  >12 publications with FKRP and Blood
 Heart Antibodies  >8 publications with FKRP and Heart
 Embryonic Tissue Antibodies  >6 publications with FKRP and Embryonic Tissue
 Nerve Antibodies  >6 publications with FKRP and Nerve
 Vascular Antibodies  >2 publications with FKRP and Vascular
 Prostate Antibodies  >1 publications with FKRP and Prostate
 Skin Antibodies  >1 publications with FKRP and Skin
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