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GLb elisa kit :: Guinea Pig Galactosidase, Beta ELISA Kit

Scan QR to view Datasheet Catalog #    MBS728593 GLb elisa kit
Unit / Price
48-Strip-Wells  /  $470 +1 FREE 8GB USB
96-Strip-Wells  /  $675 +1 FREE 8GB USB
5x96-Strip-Wells  /  $2,925 +3 FREE 8GB USB
10x96-Strip-Wells  /  $5,490 +6 FREE 8GB USB
 
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

Galactosidase, Beta (GLb), ELISA Kit

 Also Known As   

Guinea pig Galactosidase, Beta ELISA Kit

 Product Gene Name   

GLb elisa kit

[Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
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 Request for Current Manual Insert    Request Current Manual
 OMIM    611458
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 Species Reactivity    Guinea Pig
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 Preparation and Storage    Store all reagents at 2-8 degree C.
 Sample Preparation    We suggest pre-experimenting with neat (undiluted) samples, 1:2 or 1:4 dilutions. Please avoid diluting your samples more than 1:10 as it would exceed the dilution limit set for this kit. If the expected concentration of the target is beyond the detection range of the kit, please contact our technical support team
 Product Note    Our ELISA Kit assays are dynamic research tools and sometimes they may be updated and improved. If the format of this assay is important to you then please request the current manual or contact our technical support team with a presales inquiry before placing an order. We will confirm the current details of the assay. We cannot guarantee the sample manual posted online is the most current manual.
 Other Notes    Small volumes of GLb elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
 Searchable Terms for GLb purchase    MBS728593 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the Galactosidase, Beta (GLb) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing GLb. The ELISA analytical biochemical technique of the MBS728593 kit is based on GLb antibody-GLb antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect GLb antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, GLb. Appropriate sample types may include undiluted body fluids and/or tissue homogenates, secretions. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).
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NCBI/Uniprot data below describe general gene information for GLb. It may not necessarily be applicable to this product.
 NCBI GI #    119584848
 NCBI GeneID    2720
 NCBI Accession #    EAW64444.1 [Other Products]
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 UniProt Secondary Accession #    P16279; B2R7H8; B7Z6B0 [Other Products]
 UniProt Related Accession #    P16278 [Other Products]
 Molecular Weight    72,751 Da
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 NCBI Official Full Name    galactosidase, beta 1, isoform CRA_c
 NCBI Official Synonym Full Names    galactosidase, beta 1
 NCBI Official Symbol    GLB1 [Similar Products]
 NCBI Official Synonym Symbols   
EBP; ELNR1; MPS4B
[Similar Products]
 NCBI Protein Information    beta-galactosidase; lactase; acid beta-galactosidase; elastin receptor 1, 67kDa
 UniProt Protein Name    Beta-galactosidase
 UniProt Synonym Protein Names   
Acid beta-galactosidase; Lactase; Elastin receptor 1
 Protein Family    Nitrogen regulatory protein
 UniProt Gene Name    GLB1 [Similar Products]
 UniProt Synonym Gene Names    ELNR1; Lactase [Similar Products]
 UniProt Entry Name    BGAL_HUMAN
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 NCBI Summary for GLb    This gene encodes beta-galactosidase-1, a lysosomal enzyme that hydrolyzes the terminal beta-galactose from ganglioside substrates and other glycoconjugates. Defects in this gene are the cause of GM1-gangliosidosis and Morquio B syndrome. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2008]
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 UniProt Comments for GLb    GLB1: Cleaves beta-linked terminal galactosyl residues from gangliosides, glycoproteins, and glycosaminoglycans. Defects in GLB1 are the cause of GM1-gangliosidosis type 1 (GM1G1); also known as infantile GM1- gangliosidosis. GM1-gangliosidosis is an autosomal recessive lysosomal storage disease marked by the accumulation of GM1 gangliosides, glycoproteins and keratan sulfate primarily in neurons of the central nervous system. GM1G1 is characterized by onset within the first three months of life, central nervous system degeneration, coarse facial features, hepatosplenomegaly, skeletal dysmorphology reminiscent of Hurler syndrome, and rapidly progressive psychomotor deterioration. Urinary oligosaccharide levels are high. It leads to death usually between the first and second year of life. Defects in GLB1 are the cause of GM1-gangliosidosis type 2 (GM1G2); also known as late infantile/juvenile GM1- gangliosidosis. GM1G2 is characterized by onset between ages 1 and 5. The main symptom is locomotor ataxia, ultimately leading to a state of decerebration with epileptic seizures. Patients do not display the skeletal changes associated with the infantile form, but they nonetheless excrete elevated amounts of beta-linked galactose-terminal oligosaccharides. Inheritance is autosomal recessive. Defects in GLB1 are the cause of GM1-gangliosidosis type 3 (GM1G3); also known as adult or chronic GM1- gangliosidosis. GM1G3 is characterized by a variable phenotype. Patients show mild skeletal abnormalities, dysarthria, gait disturbance, dystonia and visual impairment. Visceromegaly is absent. Intellectual deficit can initially be mild or absent but progresses over time. Inheritance is autosomal recessive. Defects in GLB1 are the cause of mucopolysaccharidosis type 4B (MPS4B); also known as Morquio syndrome B. MPS4B is a form of mucopolysaccharidosis type 4, an autosomal recessive lysosomal storage disease characterized by intracellular accumulation of keratan sulfate and chondroitin-6-sulfate. Key clinical features include short stature, skeletal dysplasia, dental anomalies, and corneal clouding. Intelligence is normal and there is no direct central nervous system involvement, although the skeletal changes may result in neurologic complications. There is variable severity, but patients with the severe phenotype usually do not survive past the second or third decade of life. Belongs to the glycosyl hydrolase 35 family. 3 isoforms of the human protein are produced by alternative splicing.

Protein type: Glycan Metabolism - glycosaminoglycan degradation; EC 3.2.1.23; Lipid Metabolism - sphingolipid; Carbohydrate Metabolism - galactose; Hydrolase; Glycan Metabolism - other glycan degradation; Glycan Metabolism - glycosphingolipid biosynthesis - ganglio series

Chromosomal Location of Human Ortholog: 3p21.33

Cellular Component: Golgi apparatus; lysosomal lumen; perinuclear region of cytoplasm; cytoplasm; vacuole

Molecular Function: protein binding; galactoside binding; beta-galactosidase activity

Biological Process: keratan sulfate metabolic process; sphingolipid metabolic process; glycosaminoglycan metabolic process; dolichol-linked oligosaccharide biosynthetic process; pathogenesis; post-translational protein modification; galactose catabolic process; glycosaminoglycan catabolic process; cellular protein metabolic process; carbohydrate metabolic process; protein amino acid N-linked glycosylation via asparagine; glycosphingolipid metabolic process; cellular carbohydrate metabolic process; keratan sulfate catabolic process

Disease: Gm1-gangliosidosis, Type Iii; Mucopolysaccharidosis Type Ivb; Gm1-gangliosidosis, Type Ii; Gm1-gangliosidosis, Type I
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 Research Articles on GLb    1. The activity of serum GAL was significantly higher in colon cancer patients with a history of alcohol and nicotine dependence.
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 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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Products associated with GLb elisa kitPathways associated with GLb elisa kit
 Reference Product  PubMed Publications
 CTSA elisa kit  >6 publications with GLb and CTSA
 GALNS elisa kit  >3 publications with GLb and GALNS
 HEXA elisa kit  >2 publications with GLb and HEXA
 GLA elisa kit  >2 publications with GLb and GLA
 HEXB elisa kit  >2 publications with GLb and HEXB
 GUSB elisa kit  >2 publications with GLb and GUSB
 Products by Pathway  Pathway Diagram
 Asparagine N-linked Glycosylation Pathway antibodies  Asparagine N-linked Glycosylation Pathway Diagram
 Biosynthesis Of The N-glycan Precursor (dolichol Lipid-linked Oligosaccharide, LLO) And Transfer To A Nascent Protein Pathway antibodies  Biosynthesis Of The N-glycan Precursor (dolichol Lipid-linked Oligosaccharide, LLO) And Transfer To A Nascent Protein Pathway Diagram
 Disease Pathway antibodies  Disease Pathway Diagram
 Galactose Metabolism Pathway antibodies  Galactose Metabolism Pathway Diagram
 Galactose Metabolism Pathway antibodies  Galactose Metabolism Pathway Diagram
 Glycogen Storage Diseases Pathway antibodies  Glycogen Storage Diseases Pathway Diagram
 Glycosaminoglycan Degradation Pathway antibodies  Glycosaminoglycan Degradation Pathway Diagram
 Glycosaminoglycan Degradation Pathway antibodies  Glycosaminoglycan Degradation Pathway Diagram
 Glycosaminoglycan Metabolism Pathway antibodies  Glycosaminoglycan Metabolism Pathway Diagram
 Glycosphingolipid Biosynthesis - Ganglio Series Pathway antibodies  Glycosphingolipid Biosynthesis - Ganglio Series Pathway Diagram
Diseases associated with GLb elisa kitOrgans/Tissues associated with GLb elisa kit
 Disease Name  Pubmed Publications
 Gangliosidosis, GM1 Antibodies  >46 publications with GLb and Gangliosidosis, GM1
 Mucopolysaccharidosis IV Antibodies  >12 publications with GLb and Mucopolysaccharidosis IV
 Disease Models, Animal Antibodies  >5 publications with GLb and Disease Models, Animal
 Adenocarcinoma Antibodies  >2 publications with GLb and Adenocarcinoma
 Inflammation Antibodies  >2 publications with GLb and Inflammation
 Kidney Diseases Antibodies  >2 publications with GLb and Kidney Diseases
 Cardiovascular Diseases Antibodies  >1 publications with GLb and Cardiovascular Diseases
 Precancerous Conditions Antibodies  >1 publications with GLb and Precancerous Conditions
 Weight Loss Antibodies  >1 publications with GLb and Weight Loss
 Prostatic Diseases Antibodies  >1 publications with GLb and Prostatic Diseases
 Organ/Tissue Name  Pubmed Publications
 Blood Antibodies  >11 publications with GLb and Blood
 Skin Antibodies  >9 publications with GLb and Skin
 Brain Antibodies  >7 publications with GLb and Brain
 Kidney Antibodies  >5 publications with GLb and Kidney
 Eye Antibodies  >5 publications with GLb and Eye
 Connective Tissue Antibodies  >3 publications with GLb and Connective Tissue
 Lung Antibodies  >3 publications with GLb and Lung
 Bone Antibodies  >3 publications with GLb and Bone
 Pancreas Antibodies  >3 publications with GLb and Pancreas
 Placenta Antibodies  >2 publications with GLb and Placenta
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