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NFU1 elisa kit :: Human NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) ELISA Kit

Scan QR to view Datasheet Catalog #    MBS9343389 NFU1 elisa kit
Unit / Price
48-Strip-Wells  /  $470 +1 FREE 8GB USB
96-Strip-Wells  /  $680 +1 FREE 8GB USB
5x96-Strip-Wells  /  $3,100 +3 FREE 8GB USB
10x96-Strip-Wells  /  $6,095 +7 FREE 8GB USB
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae), ELISA Kit

 Also Known As   

Human NFU1 iron-sulfur cluster scaffold homolog, mitochondrial, NFU1 ELISA Kit

 Product Synonym Names    Human NFU1 iron-sulfur cluster scaffold homolog; mitochondrial (NFU1) ELISA kit; CGI-33; HIRIP5; MGC142252; MGC142254; NIFUC; Nfu; NifU; HIRA interacting protein 5; HIRA-interacting protein 5; NifU-like C-terminal domain containing; OTTHUMP00000202180; iron-sulfur cluster scaffold p; NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae)
 Product Gene Name   

NFU1 elisa kit

[Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
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 Request for Current Manual Insert    Request Current Manual
 OMIM    608100
 3D Structure    ModBase 3D Structure for Q9UMS0
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 Species Reactivity    Human
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 Preparation and Storage    Store all reagents at 2-8 degree C
 Product Note    Our ELISA Kit assays are dynamic research tools and sometimes they may be updated and improved. If the format of this assay is important to you then please request the current manual or contact our technical support team with a presales inquiry before placing an order. We will confirm the current details of the assay. We cannot guarantee the sample manual posted online is the most current manual.
 Other Notes    Small volumes of NFU1 elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
 Searchable Terms for NFU1 purchase    MBS9343389 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing NFU1. The ELISA analytical biochemical technique of the MBS9343389 kit is based on NFU1 antibody-NFU1 antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect NFU1 antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, NFU1. Appropriate sample types may include undiluted body fluids and/or tissue homogenates, secretions. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).
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NCBI/Uniprot data below describe general gene information for NFU1. It may not necessarily be applicable to this product.
 NCBI GI #    50593021
 NCBI GeneID    27247
 NCBI Accession #    NP_001002755.1 [Other Products]
 NCBI GenBank Nucleotide #    NM_001002755.2 [Other Products]
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 UniProt Primary Accession #    Q9UMS0 [Other Products]
 UniProt Secondary Accession #    Q53QE5; Q6VNZ8; Q7Z5B1; Q7Z5B2; Q9Y322; B4DUL9 [Other Products]
 UniProt Related Accession #    Q9UMS0 [Other Products]
 Molecular Weight    28,463 Da
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 NCBI Official Full Name    NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform 2
 NCBI Official Synonym Full Names    NFU1 iron-sulfur cluster scaffold
 NCBI Official Symbol    NFU1 [Similar Products]
 NCBI Official Synonym Symbols   
[Similar Products]
 NCBI Protein Information    NFU1 iron-sulfur cluster scaffold homolog, mitochondrial; HIRA-interacting protein 5; iron-sulfur cluster scaffold protein; NifU-like C-terminal domain containing
 UniProt Protein Name    NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
 UniProt Synonym Protein Names   
HIRA-interacting protein 5
 Protein Family    NifU-like protein
 UniProt Gene Name    NFU1 [Similar Products]
 UniProt Synonym Gene Names    HIRIP5; CGI-33 [Similar Products]
 UniProt Entry Name    NFU1_HUMAN
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 NCBI Summary for NFU1    This gene encodes a protein that is localized to mitochondria and plays a critical role in iron-sulfur cluster biogenesis. The encoded protein assembles and transfers 4Fe-4S clusters to target apoproteins including succinate dehydrogenase and lipoic acid synthase. Mutations in this gene are a cause of multiple mitochondrial dysfunctions syndrome-1, and pseudogenes of this gene are located on the short arms of chromosomes 1 and 3. Alternatively spliced transcript variants encoding multiple isoforms have been observed for this gene. [provided by RefSeq, Dec 2011]
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 UniProt Comments for NFU1    NFU1: Iron-sulfur cluster scaffold protein which can assemble [4Fe-2S] clusters and deliver them to target proteins. Defects in NFU1 are the cause of multiple mitochondrial dysfunctions syndrome type 1 (MMDS1). A severe disorder of systemic energy metabolism, resulting in weakness, respiratory failure, lack of neurologic development, lactic acidosis, hyperglycinemia and early death. Some patients show failure to thrive, pulmonary hypertension, hypotonia and irritability. Biochemical features include severe combined deficiency of the 2-oxoacid dehydrogenases, defective lipoic acid synthesis and reduction in activity of mitochondrial respiratory chain complexes. Belongs to the NifU family. 3 isoforms of the human protein are produced by alternative splicing.

Protein type: Mitochondrial

Chromosomal Location of Human Ortholog: 2p15-p13

Cellular Component: nucleoplasm; mitochondrion; cytoplasm; nucleus; cytosol

Molecular Function: protein binding; iron ion binding; 4 iron, 4 sulfur cluster binding

Biological Process: iron-sulfur cluster assembly

Disease: Multiple Mitochondrial Dysfunctions Syndrome 1
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 Research Articles on NFU1    1. This study provides new insights into the molecular bases of NFU1 disease.
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 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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Products associated with NFU1 elisa kitDiseases associated with NFU1 elisa kit
 Reference Product  PubMed Publications
 EPM2A elisa kit  >2 publications with NFU1 and EPM2A
 HIRA elisa kit  >1 publications with NFU1 and HIRA
 Disease Name  Pubmed Publications
 Infection Antibodies  >2 publications with NFU1 and Infection
 Shock Antibodies  >2 publications with NFU1 and Shock
 Brain Diseases Antibodies  >2 publications with NFU1 and Brain Diseases
 Disease Models, Animal Antibodies  >1 publications with NFU1 and Disease Models, Animal
 Acidosis Antibodies  >1 publications with NFU1 and Acidosis
 Hypertension Antibodies  >1 publications with NFU1 and Hypertension
 Vascular Diseases Antibodies  >1 publications with NFU1 and Vascular Diseases
Organs/Tissues associated with NFU1 elisa kit
 Organ/Tissue Name  Pubmed Publications
 Kidney Antibodies  >1 publications with NFU1 and Kidney
 Lung Antibodies  >1 publications with NFU1 and Lung
 Brain Antibodies  >1 publications with NFU1 and Brain
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