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CTNS elisa kit :: Monkey Cystinosin (CTNS) ELISA Kit

Scan QR to view Datasheet Catalog #    MBS7222142 CTNS elisa kit
Unit / Price
48-Strip-Wells  /  $455 +1 FREE 8GB USB
96-Strip-Wells  /  $660 +1 FREE 8GB USB
5x96-Strip-Wells  /  $2,925 +3 FREE 8GB USB
10x96-Strip-Wells  /  $5,490 +6 FREE 8GB USB
 
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

Cystinosin (CTNS), ELISA Kit

 Also Known As   

Monkey Cystinosin (CTNS) ELISA Kit

 Product Gene Name   

CTNS elisa kit

[Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
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 Request for Current Manual Insert    Request Current Manual
 Species Reactivity    Monkey
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 Samples    Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
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 Preparation and Storage    Store all reagents at 2-8 degree C.
 Sample Preparation    We suggest pre-experimenting with neat (undiluted) samples, 1:2 or 1:4 dilutions. Please avoid diluting your samples more than 1:10 as it would exceed the dilution limit set for this kit. If the expected concentration of the target is beyond the detection range of the kit, please contact our technical support team
 Product Note    Our ELISA Kit assays are dynamic research tools and sometimes they may be updated and improved. If the format of this assay is important to you then please request the current manual or contact our technical support team with a presales inquiry before placing an order. We will confirm the current details of the assay. We cannot guarantee the sample manual posted online is the most current manual.
 Other Notes    Small volumes of CTNS elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
 Searchable Terms for CTNS purchase    MBS7222142 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the Cystinosin (CTNS) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing CTNS. The ELISA analytical biochemical technique of the MBS7222142 kit is based on CTNS antibody-CTNS antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect CTNS antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, CTNS. Appropriate sample types may include undiluted body fluids and/or tissue homogenates, secretions such as Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).
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NCBI/Uniprot data below describe general gene information for CTNS. It may not necessarily be applicable to this product.
 NCBI GI #    13752577
 NCBI GeneID    83429
 NCBI Accession #    NP_112541.1 [Other Products]
 NCBI GenBank Nucleotide #    NM_031251.4 [Other Products]
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 UniProt Related Accession #    P57757 [Other Products]
 Molecular Weight    42,203 Da
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 NCBI Official Full Name    cystinosin
 NCBI Official Synonym Full Names    cystinosis, nephropathic
 NCBI Official Symbol    Ctns [Similar Products]
 NCBI Official Synonym Symbols   
AI195360; AW049661
[Similar Products]
 NCBI Protein Information    cystinosin
 UniProt Protein Name    Cystinosin
 Protein Family    Cystinosin
 UniProt Gene Name    Ctns [Similar Products]
 UniProt Entry Name    CTNS_MOUSE
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 UniProt Comments for CTNS    CTNS: Thought to transport cystine out of lysosomes. Defects in CTNS are the cause of cystinosis nephropathic type (CTNS). It is a form of cystinosis, a lysosomal storage disease due to defective transport of cystine across the lysosomal membrane. This results in cystine accumulation and crystallization in the cells causing widespread tissue damage. The classical nephropathic form has onset in the first year of life and is characterized by a polyuro-polydipsic syndrome, marked height-weight growth delay, generalized impaired proximal tubular reabsorptive capacity, with severe fluid-electrolyte balance alterations, renal failure, ocular symptoms and other systemic complications. Defects in CTNS are the cause of cystinosis adult non- nephropathic type (CTNSANN). It is a form of cystinosis, a lysosomal storage disease due to defective transport of cystine across the lysosomal membrane. This results in cystine accumulation and crystallization in the cells causing widespread tissue damage. Cystinosis adult non-nephropathic type is characterized by ocular features and a benigne course. Patients manifest mild photophobia due to conjunctival and corneal cystine crystals. Defects in CTNS are the cause of cystinosis late-onset juvenile or adolescent nephropathic type (CTNSJAN). It is a form of cystinosis, a lysosomal storage disease due to defective transport of cystine across the lysosomal membrane. This results in cystine accumulation and crystallization in the cells causing widespread tissue damage. Late-onset juvenile or adolescent nephropathic cystinosis manifests itself first at age 10 to 12 years with proteinuria due to glomerular damage rather than with the manifestations of tubular damage that occur first in infantile cystinosis. There is no excess amino aciduria and stature is normal. Photophobia, late development of pigmentary retinopathy, and chronic headaches are features. Belongs to the cystinosin family. 2 isoforms of the human protein are produced by alternative splicing.

Protein type: Membrane protein, multi-pass; Membrane protein, integral

Cellular Component: intermediate filament cytoskeleton; intracellular membrane-bound organelle; membrane; lysosomal membrane; lysosome; late endosome; plasma membrane; integral to membrane

Molecular Function: L-cystine transmembrane transporter activity

Biological Process: grooming behavior; melanin biosynthetic process; lens development in camera-type eye; ATP metabolic process; glutathione metabolic process; long-term memory; transport; L-cystine transport; visual learning; brain development; cognition; adult walking behavior
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 Research Articles on CTNS    1. The onset of Fanconi syndrome in knockout mice is between 3 and 6 months of age with structural and functional changes in proximal tubular cells (PTCs), with focus on endocytosis of ultrafiltrated disulfide-rich proteins as a key source of cystine.
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 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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Pathways associated with CTNS elisa kitDiseases associated with CTNS elisa kit
 Products by Pathway  Pathway Diagram
 Lysosome Pathway antibodies  Lysosome Pathway Diagram
 Lysosome Pathway antibodies  Lysosome Pathway Diagram
 Disease Name  Pubmed Publications
 Cystinosis Antibodies  >1261 publications with CTNS and Cystinosis
 Male Urogenital Diseases Antibodies  >471 publications with CTNS and Male Urogenital Diseases
 Nervous System Diseases Antibodies  >175 publications with CTNS and Nervous System Diseases
 Endocrine System Diseases Antibodies  >117 publications with CTNS and Endocrine System Diseases
 Liver Diseases Antibodies  >50 publications with CTNS and Liver Diseases
 Growth Disorders Antibodies  >36 publications with CTNS and Growth Disorders
 Atrophy Antibodies  >27 publications with CTNS and Atrophy
 Bone Diseases, Developmental Antibodies  >26 publications with CTNS and Bone Diseases, Developmental
 Heart Diseases Antibodies  >24 publications with CTNS and Heart Diseases
 Autoimmune Diseases Antibodies  >22 publications with CTNS and Autoimmune Diseases
Organs/Tissues associated with CTNS elisa kit
 Organ/Tissue Name  Pubmed Publications
 Kidney Antibodies  >486 publications with CTNS and Kidney
 Blood Antibodies  >289 publications with CTNS and Blood
 Eye Antibodies  >184 publications with CTNS and Eye
 Bone Antibodies  >96 publications with CTNS and Bone
 Skin Antibodies  >66 publications with CTNS and Skin
 Brain Antibodies  >64 publications with CTNS and Brain
 Heart Antibodies  >31 publications with CTNS and Heart
 Intestine Antibodies  >21 publications with CTNS and Intestine
 Spleen Antibodies  >16 publications with CTNS and Spleen
 Connective Tissue Antibodies  >10 publications with CTNS and Connective Tissue
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