Antibody Protein ELISA Kit from MyBioSource header Telephone 1.858.633.0165          
1.855.MyBioSource
Fax 1.858.633.0166    Email sales@mybiosource.com 
tel/fax
menu1 Home Products Ordering Company Help menu7
bottom
   MyBioSource rightarrow ELISA Kit rightarrow alphaGAL rightarrow Rabbit alphaGAL  rightarrow LOG IN  rightarrow MY ACCOUNT  rightarrow CART CONTENTS  rightarrow CHECKOUT 
horiz bar
MyBioSource Menu separator
separator
ELISA Kit ELISA Kit
CLIA Kit CLIA Kit
PCR Kit PCR Kit
Monoclonal Antibody Monoclonal Antibody
Polyclonal Antibody Polyclonal Antibody
Secondary Antibody Secondary Antibody
Antigen Antigen
Biochemical Biochemical
cDNA Clone cDNA Clone
siRNA siRNA
Peptide Peptide
Recombinant/Purified Protein Rec./Purified Protein

Custom ELISA Kit Custom ELISA Kit
Custom Protein Custom Protein
Custom Antibody Custom Antibody
Antibody Matched Pairs Antibody Matched Pairs
Antibody & Corresponding Blocking Peptide Pairs Antibody Peptide Pairs
Phospho-Specific Antibodies Phospho Antibodies
Products by Disease Products by Disease
Products by Pathway Products by Pathway
Products by Tissue Products by Tissue

arrow Advanced Search
arrow Submit Technical Q&A
arrow International Distributors
arrow Contact Us
separator
Our Best Sellers moreseparator
separator
 • High Mobility Group Box1 Protein (HMGB1) ELISA Kit
 • Anti-Survivin Antibody ELISA Kit
 • CD51 Antibody
 • PECAM1 Antibody
 • g3 Calcium Channel (CACNG3) Antibody
 • CD1D Antibody
 • thyroid stimulating hormone receptor antibody (TSHR Ab) ELISA Kit
 • 2-Oxoisovalerate Dehydrogenase Subunit Alpha, Mitochondrial ... ELISA Kit
 • KCTD5 Recombinant Protein
 • Anion exchange protein 2 (SLC4A2) Recombinant Protein
 • alpha-fetoprotein (AFP) ELISA Kit
 • ABL1 Antibody
 • vacuolar protein sorting 37 homolog C (S. cerevisiae) (VPS3... ELISA Kit
 • Integrin alphaV beta 1 (ITGB1) Recombinant Protein
 downarrow more ...
separator
separator
DatasheetFull DatasheetPrinter Friendly DatasheetPrint This DatasheetAdd to Compare ListHave Questions? Ask UsRequest for a Quotation today

alphaGAL elisa kit :: Rabbit alpha-Galactosidase ELISA Kit

Scan QR to view Datasheet Catalog #    MBS740630 alphaGAL elisa kit
Unit / Price
48-Strip-Wells  /  $470 +1 FREE 8GB USB
96-Strip-Wells  /  $675 +1 FREE 8GB USB
 
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

alpha-Galactosidase (alphaGAL), ELISA Kit

 Also Known As   

Rabbit alpha-Galactosidase ELISA Kit

 Product Synonym Names    Rabbit a-Galactosidase ELISA Kit
 Product Gene Name   

alphaGAL elisa kit

[Similar Products]
 Product Synonym Gene Name    aGAL [Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
Table BarTOPTable Bar
 Request for Manual Insert    Request Manual
 OMIM    gene 301500
Section Bar
 Species Reactivity    Rabbit
Section Bar
Section Bar
 Preparation and Storage    Store all reagents at 2-8 degree C.
 Sample Preparation    We suggest pre-experimenting with neat (undiluted) samples, 1:2 or 1:4 dilutions. Please avoid diluting your samples more than 1:10 as it would exceed the dilution limit set for this kit. If the expected concentration of the target is beyond the detection range of the kit, please contact technical support.
 Other Notes    Small volumes of alphaGAL elisa kit vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
 Searchable Terms for alphaGAL purchase    MBS740630 is a ready-to-use microwell, strip plate ELISA (enzyme-linked immunosorbent assay) Kit for analyzing the presence of the alpha-Galactosidase (alphaGAL) ELISA Kit target analytes in biological samples. The concentration gradients of the kit standards or positive controls render a theoretical kit detection range in biological research samples containing alphaGAL. The ELISA analytical biochemical technique of the MBS740630 kit is based on alphaGAL antibody-alphaGAL antigen interactions (immunosorbency) and an HRP colorimetric detection system to detect alphaGAL antigen targets in samples. The ELISA Kit is designed to detect native, not recombinant, alphaGAL. Appropriate sample types may include undiluted human body fluids and/or tissue homogenates, secretions. Quality control assays assessing reproducibility identified the intra-assay CV (%) and inter-assay CV(%).
Table BarTOPTable Bar
 Product Categories/Family for alphaGAL elisa kit    Cardiovascular
NCBI/Uniprot data below describe general gene information for alphaGAL. It may not necessarily be applicable to this product.
 NCBI GI #    553299
 NCBI GeneID    2717
 NCBI Accession #    AAA52514.1 [Other Products]
Section Bar
 UniProt Secondary Accession #    Q6LER7 [Other Products]
 UniProt Related Accession #    P06280 [Other Products]
 Molecular Weight    48,767 Da
Table BarTOPTable Bar
 NCBI Official Full Name    alpha-galactosidase, partial
 NCBI Official Synonym Full Names    galactosidase, alpha
 NCBI Official Symbol    GLA [Similar Products]
 NCBI Official Synonym Symbols   
GALA
[Similar Products]
 NCBI Protein Information    alpha-galactosidase A; melibiase; alpha-gal A; agalsidase alfa; alpha-D-galactosidase A; alpha-D-galactoside galactohydrolase 1
 UniProt Protein Name    Alpha-galactosidase A
 UniProt Synonym Protein Names   
Alpha-D-galactosidase A; Alpha-D-galactoside galactohydrolase; Melibiase; INN: Agalsidase
 Protein Family    Alpha-galactosidase
 UniProt Gene Name    GLA [Similar Products]
 UniProt Entry Name    AGAL_HUMAN
Section Bar
 NCBI Summary for alphaGAL    This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008]
Section Bar
 UniProt Comments for alphaGAL    GLA: Defects in GLA are the cause of Fabry disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism. FD patients show systemic accumulation of globotriaoslyceramide (Gb3) and related glycosphingolipids in the plasma and cellular lysosomes throughout the body. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities. Belongs to the glycosyl hydrolase 27 family.

Protein type: Lipid Metabolism - glycerolipid; Lipid Metabolism - sphingolipid; Carbohydrate Metabolism - galactose; Glycan Metabolism - glycosphingolipid biosynthesis - globo series; EC 3.2.1.22; Hydrolase

Chromosomal Location of Human Ortholog: Xq22

Cellular Component: Golgi apparatus; lysosomal lumen; lysosome; cytoplasm; extracellular region

Molecular Function: protein binding; protein homodimerization activity; hydrolase activity; alpha-galactosidase activity; galactoside binding; catalytic activity; receptor binding

Biological Process: sphingolipid metabolic process; negative regulation of nitric-oxide synthase activity; glycoside catabolic process; negative regulation of nitric oxide biosynthetic process; glycosphingolipid catabolic process; glycosylceramide catabolic process; glycosphingolipid metabolic process; oligosaccharide metabolic process

Disease: Fabry Disease
Table BarTOPTable Bar
 Research Articles on alphaGAL    1. residues important for expression of the GLA activity
Table BarTOPTable Bar
 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
Table BarTOPTable Bar
Products related to Rabbit alpha-Galactosidase ELISA Kit
 Catalog #  Product Name  Catalog #  Product Name
 MBS1294826  Recombinant Neosartorya fumigata Probable alpha-galactosidase B (aglB)  MBS1442408  Recombinant Alpha-galactosidase (MEL)
 MBS006436  Goose alpha-Galactosidase ELISA Kit  MBS8243211  Alpha-Galactosidase Microplate Assay Kit
 MBS2601112  Rabbit alpha-galactosidase (alpha-GAL) ELISA Kit  MBS741983  Sheep alpha-Galactosidase ELISA Kit
 MBS1113401  Recombinant Capsicum annuum var. annuum Alpha-galactosidase  MBS049414  Duck alpha-Galactosidase ELISA Kit
 MBS1441701  Recombinant Torulaspora delbrueckii Alpha-galactosidase (MEL)  MBS739885  Guinea pig alpha-Galactosidase ELISA Kit
Products associated with alphaGAL elisa kitPathways associated with alphaGAL elisa kit
 Reference Product  PubMed Publications
 GAA elisa kit  >8 publications with alphaGAL and GAA
 ARSA elisa kit  >4 publications with alphaGAL and ARSA
 HEXA elisa kit  >3 publications with alphaGAL and HEXA
 GALC elisa kit  >3 publications with alphaGAL and GALC
 GLB1 elisa kit  >2 publications with alphaGAL and GLB1
 HEXB elisa kit  >1 publications with alphaGAL and HEXB
 Products by Pathway  Pathway Diagram
 Galactose Metabolism Pathway antibodies  Galactose Metabolism Pathway Diagram
 Galactose Metabolism Pathway antibodies  Galactose Metabolism Pathway Diagram
 Glycerolipid Metabolism Pathway antibodies  Glycerolipid Metabolism Pathway Diagram
 Glycerolipid Metabolism Pathway antibodies  Glycerolipid Metabolism Pathway Diagram
 Glycosphingolipid Biosynthesis - Globo Series Pathway antibodies  Glycosphingolipid Biosynthesis - Globo Series Pathway Diagram
 Glycosphingolipid Biosynthesis - Globo Series Pathway antibodies  Glycosphingolipid Biosynthesis - Globo Series Pathway Diagram
 Glycosphingolipid Metabolism Pathway antibodies  Glycosphingolipid Metabolism Pathway Diagram
 Lysosome Pathway antibodies  Lysosome Pathway Diagram
 Lysosome Pathway antibodies  Lysosome Pathway Diagram
 Metabolism Pathway antibodies  Metabolism Pathway Diagram
Diseases associated with alphaGAL elisa kitOrgans/Tissues associated with alphaGAL elisa kit
 Disease Name  Pubmed Publications
 Cardiovascular Diseases Antibodies  >1196 publications with alphaGAL and Cardiovascular Diseases
 Nervous System Diseases Antibodies  >960 publications with alphaGAL and Nervous System Diseases
 Heart Diseases Antibodies  >415 publications with alphaGAL and Heart Diseases
 Inflammation Antibodies  >331 publications with alphaGAL and Inflammation
 Disease Models, Animal Antibodies  >262 publications with alphaGAL and Disease Models, Animal
 Kidney Diseases Antibodies  >249 publications with alphaGAL and Kidney Diseases
 Hypertension Antibodies  >237 publications with alphaGAL and Hypertension
 Fabry Disease Antibodies  >207 publications with alphaGAL and Fabry Disease
 Necrosis Antibodies  >171 publications with alphaGAL and Necrosis
 Pain Antibodies  >164 publications with alphaGAL and Pain
 Organ/Tissue Name  Pubmed Publications
 Blood Antibodies  >2113 publications with alphaGAL and Blood
 Bone Antibodies  >1277 publications with alphaGAL and Bone
 Vascular Antibodies  >741 publications with alphaGAL and Vascular
 Heart Antibodies  >554 publications with alphaGAL and Heart
 Brain Antibodies  >507 publications with alphaGAL and Brain
 Connective Tissue Antibodies  >505 publications with alphaGAL and Connective Tissue
 Kidney Antibodies  >396 publications with alphaGAL and Kidney
 Liver Antibodies  >270 publications with alphaGAL and Liver
 Skin Antibodies  >193 publications with alphaGAL and Skin
 Nerve Antibodies  >152 publications with alphaGAL and Nerve
Table BarTOPTable Bar
horiz bar
 SSL   Follow us on Facebook Follow us onTwitter Follow us on Google Plus Connect us on LinkedIn Subscribe to our RSS Feed for latest products and special promotions