NP_036914.1
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NCBI GenBank Nucleotide #
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UniProt Primary Accession #
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UniProt Related Accession #
Molecular Weight
50,164 Da
NCBI Official Full Name
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
NCBI Official Synonym Full Names
branched chain ketoacid dehydrogenase E1, alpha polypeptide
NCBI Official Synonym Symbols
NCBI Protein Information
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
UniProt Protein Name
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
UniProt Synonym Protein Names
Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain; BCKDE1A; BCKDH E1-alpha
UniProt Synonym Gene Names
NCBI Summary for Bckdha
plays a role in the conversion of 3-methyl-2-oxobutanoate and lipoamide to S-(2-methylpropanoyl)dihydrolipoamide and CO2 [RGD, Feb 2006]
UniProt Comments for Bckdha
The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO2. It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).MiscellaneousBound potassium ions stabilize the protein structure.
Research Articles on Bckdha
Precautions
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Disclaimer
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Pathways associated with Bckdha recombinant protein
Diseases associated with Bckdha recombinant protein
Organs/Tissues associated with Bckdha recombinant protein
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