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SGSH recombinant protein :: N-sulphoglucosamine sulphohydrolase (SGSH) Recombinant Protein

Scan QR to view Datasheet Catalog #    MBS965238 SGSH recombinant protein
Unit / Price
0.05 mg (E-Coli)  /  $900 +1 FREE 8GB USB
0.05 mg (Baculovirus)  /  $1,115 +1 FREE 8GB USB
0.2 mg (E-Coli)  /  $1,210 +1 FREE 8GB USB
0.2 mg (Yeast)  /  $1,330 +1 FREE 8GB USB
0.5 mg (E-Coli)  /  $1,330 +1 FREE 8GB USB
0.05 mg (Mammalian-Cell)  /  $1,360 +1 FREE 8GB USB
0.1 mg (Baculovirus)  /  $1,410 +1 FREE 8GB USB
0.5 mg (Yeast)  /  $1,505 +1 FREE 8GB USB
1 mg (E-Coli)  /  $1,895 +2 FREE 8GB USB
0.5 mg (Baculovirus)  /  $2,025 +2 FREE 8GB USB
0.1 mg (Mammalian-Cell)  /  $2,055 +2 FREE 8GB USB
1 mg (Yeast)  /  $2,290 +2 FREE 8GB USB
1 mg (Baculovirus)  /  $2,665 +3 FREE 8GB USB
 
 Go to:   rightarrow  Product Names   rightarrow Product Info   rightarrow Accession #s   rightarrow Product Desc   rightarrow Diseases/Tissues/Pathways   rightarrow Applications   rightarrow References 
 Product Name   

N-sulphoglucosamine sulphohydrolase (SGSH), Recombinant Protein

★Popular Item★
 Also Known As   

Recombinant Human N-sulphoglucosamine sulphohydrolase (SGSH)

 Product Gene Name   

SGSH recombinant protein

[Similar Products]
 Research Use Only    For Research Use Only. Not for use in diagnostic procedures.
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 Sequence Positions    21-502aa, Full Length of Mature Protein
 Sequence    RPRNALLLLA DDGGFESGAY NNSAIATPHL DALARRSLLF RNAFTSVSSC SPSRASLLTG LPQHQNGMYG LHQDVHHFNS FDKVRSLPLL LSQAGVRTGI IGKKHVGPET VYPFDFAYTE ENGSVLQVGR NITRIKLLVR KFLQTQDDRP FFLYVAFHDP HRCGHSQPQY GTFCEKFGNG ESGMGRIPDW TPQAYDPLDV LVPYFVPNTP AARADLAAQY TTVGRMDQGV GLVLQELRDA GVLNDTLVIF TSDNGIPFPS GRTNLYWPGT AEPLLVSSPE HPKRWGQVSE AYVSLLDLTP TILDWFSIPY PSYAIFGSKT IHLTGRSLLP ALEAEPLWAT VFGSQSHHEV TMSYPMRSVQ HRHFRLVHNL NFKMPFPIDQ DFYVSPTFQD LLNRTTAGQP TGWYKDLRHY YYRARWELYD RSRDPHETQN LATDPRFAQL LEMLRDQLAK WQWETHDPWV CAPDGVLEEK LSPQCQPLHN EL
 OMIM    252900
 3D Structure    ModBase 3D Structure for P51688
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 Host    E Coli or Yeast or Baculovirus or Mammalian Cell
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 Purity/Purification    >85% (SDS-PAGE) (lot specific)
 Form/Format    Liquid containing glycerol
 Tag Information    This protein contains an N-terminal tag and may also contain a C-terminal tag. Tag types are determined by various factors including tag-protein stability, please inquire for tag information.
 Sterility    Sterile filter available upon request.
 Endotoxin    Low endotoxin available upon request.
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 Species    Human
 Storage Buffer    Tris-based buffer, 50% glycerol
 Tag Information    Tag type will be determined during the manufacturing process
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 Preparation and Storage    Store at -20 degrees C. For long-term storage, store at -20 degrees C or -80 degrees C. Store working aliquots at 4 degrees C for up to one week. Repeated freezing and thawing is not recommended.
 ISO Certification    Manufactured in an ISO 9001:2008 Certified Laboratory.
 Other Notes    Small volumes of SGSH recombinant protein vial(s) may occasionally become entrapped in the seal of the product vial during shipment and storage. If necessary, briefly centrifuge the vial on a tabletop centrifuge to dislodge any liquid in the container`s cap. Certain products may require to ship with dry ice and additional dry ice fee may apply.
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Related Product Information for SGSH recombinant protein

   This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
NCBI/Uniprot data below describe general gene information for SGSH. It may not necessarily be applicable to this product.
 NCBI GI #    4506919
 NCBI GeneID    6448
 NCBI Accession #    NP_000190.1 [Other Products]
 NCBI GenBank Nucleotide #    NM_000199.4 [Other Products]
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 UniProt Primary Accession #    P51688 [Other Products]
 UniProt Secondary Accession #    A8K5E2 [Other Products]
 UniProt Related Accession #    P51688 [Other Products]
 Molecular Weight    56,695 Da
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 NCBI Official Full Name    N-sulphoglucosamine sulphohydrolase isoform 1
 NCBI Official Synonym Full Names    N-sulfoglucosamine sulfohydrolase
 NCBI Official Symbol    SGSH [Similar Products]
 NCBI Official Synonym Symbols   
HSS; SFMD; MPS3A
[Similar Products]
 NCBI Protein Information    N-sulphoglucosamine sulphohydrolase
 UniProt Protein Name    N-sulphoglucosamine sulphohydrolase
 UniProt Synonym Protein Names   
Sulfoglucosamine sulfamidase; Sulphamidase
 Protein Family    N-sulphoglucosamine sulphohydrolase
 UniProt Gene Name    SGSH [Similar Products]
 UniProt Synonym Gene Names    HSS [Similar Products]
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 NCBI Summary for SGSH    This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
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 UniProt Comments for SGSH    Catalyzes a step in lysosomal heparan sulfate degradation.
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 Research Articles on SGSH    1. CSF enzyme activity levels for either SGSH (in MPS IIIA subjects) or NAGLU (in MPS IIIB) significantly differed from normal controls. Several other behavioral or functional measures were found to be uninformative in this population, including timed functional motor tests.
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 Precautions    All of MyBioSource's Products are for scientific laboratory research purposes and are not for diagnostic, therapeutics, prophylactic or in vivo use. Through your purchase, you expressly represent and warrant to MyBioSource that you will properly test and use any Products purchased from MyBioSource in accordance with industry standards. MyBioSource and its authorized distributors reserve the right to refuse to process any order where we reasonably believe that the intended use will fall outside of our acceptable guidelines.
 Disclaimer    While every efforts were made to ensure the accuracy of the information provided in this datasheet, MyBioSource will not be liable for any omissions or errors contained herein. MyBioSource reserves the right to make changes to this datasheet at any time without prior notice.

It is the responsibility of the customer to report product performance issues to MyBioSource within 30 days of receipt of the product. Please visit our Terms & Conditions page for more information.
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Products associated with SGSH recombinant proteinPathways associated with SGSH recombinant protein
 Reference Product  PubMed Publications
 NAGLU recombinant protein  >6 publications with SGSH and NAGLU
 IDUA recombinant protein  >3 publications with SGSH and IDUA
 GNS recombinant protein  >2 publications with SGSH and GNS
 SUMF1 recombinant protein  >2 publications with SGSH and SUMF1
 HGSNAT recombinant protein  >2 publications with SGSH and HGSNAT
 Products by Pathway  Pathway Diagram
 Defective B3GAT3 Causes JDSSDHD Pathway antibodies  Defective B3GAT3 Causes JDSSDHD Pathway Diagram
 Defective B4GALT1 Causes B4GALT1-CDG (CDG-2d) Pathway antibodies  Defective B4GALT1 Causes B4GALT1-CDG (CDG-2d) Pathway Diagram
 Defective B4GALT7 Causes EDS, Progeroid Type Pathway antibodies  Defective B4GALT7 Causes EDS, Progeroid Type Pathway Diagram
 Defective CHST14 Causes EDS, Musculocontractural Type Pathway antibodies  Defective CHST14 Causes EDS, Musculocontractural Type Pathway Diagram
 Defective CHST3 Causes SEDCJD Pathway antibodies  Defective CHST3 Causes SEDCJD Pathway Diagram
 Defective CHST6 Causes MCDC1 Pathway antibodies  Defective CHST6 Causes MCDC1 Pathway Diagram
 Defective CHSY1 Causes TPBS Pathway antibodies  Defective CHSY1 Causes TPBS Pathway Diagram
 Defective EXT1 Causes Exostoses 1, TRPS2 And CHDS Pathway antibodies  Defective EXT1 Causes Exostoses 1, TRPS2 And CHDS Pathway Diagram
 Defective EXT2 Causes Exostoses 2 Pathway antibodies  Defective EXT2 Causes Exostoses 2 Pathway Diagram
 Defective PAPSS2 Causes SEMD-PA Pathway antibodies  Defective PAPSS2 Causes SEMD-PA Pathway Diagram
Diseases associated with SGSH recombinant proteinOrgans/Tissues associated with SGSH recombinant protein
 Disease Name  Pubmed Publications
 Mucopolysaccharidosis III Antibodies  >22 publications with SGSH and Mucopolysaccharidosis III
 Death Antibodies  >7 publications with SGSH and Death
 Splenomegaly Antibodies  >1 publications with SGSH and Splenomegaly
 Hypertrophy Antibodies  >1 publications with SGSH and Hypertrophy
 Body Weight Changes Antibodies  >1 publications with SGSH and Body Weight Changes
 Immune System Diseases Antibodies  >1 publications with SGSH and Immune System Diseases
 Atrophy Antibodies  >1 publications with SGSH and Atrophy
 Inflammation Antibodies  >1 publications with SGSH and Inflammation
 Organ/Tissue Name  Pubmed Publications
 Brain Antibodies  >15 publications with SGSH and Brain
 Blood Antibodies  >7 publications with SGSH and Blood
 Liver Antibodies  >3 publications with SGSH and Liver
 Bone Antibodies  >2 publications with SGSH and Bone
 Vascular Antibodies  >1 publications with SGSH and Vascular
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