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Isobutyryl-CoA dehydrogenase

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Has very high activity toward isobutyryl-CoA. Is an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Plays a role in transcriptional coactivation within the ARC complex.

Below are the list of possible Isobutyryl-CoA dehydrogenase products. If you cannot find the target and/or product is not available in our catalog, please click here to contact us and request the product or submit your request for custom elisa kit production, custom recombinant protein production or custom antibody production. Custom ELISA Kits, Recombinant Proteins and Antibodies can be designed, manufactured and produced according to the researcher's specifications.
 

Isobutyryl-CoA dehydrogenase

 Isobutyryl-CoA dehydrogenase ELISA Kit
 Isobutyryl-CoA dehydrogenase Recombinant
 Isobutyryl-CoA dehydrogenase Antibody
Also known as Isobutyryl-CoA dehydrogenase, mitochondrial (Activator-recruited cofactor 42 kDa component) (ARC42) (Acyl-CoA dehydrogenase family member 8) (ACAD-8).
ACAD8: Has very high activity toward isobutyryl-CoA. Is an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Plays a role in transcriptional coactivation within the ARC complex. Defects in ACAD8 are the cause of isobutyryl-CoA dehydrogenase deficiency (IBDD). The symptoms of IBDD generally appear until late in infancy or in childhood and can include poor feeding and growth (failure to thrive), a weakened and enla
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rged heart (dilated cardiomyopathy), seizures, and low numbers of red blood cells (anemia). Belongs to the acyl-CoA dehydrogenase family.

Protein type: Amino Acid Metabolism - valine, leucine and isoleucine degradation; EC 1.3.99.-; Mitochondrial; Oxidoreductase

Chromosomal Location of Human Ortholog: 11q25

Cellular Component: mitochondrial matrix; mitochondrion

Molecular Function: acyl-CoA binding; acyl-CoA dehydrogenase activity; electron carrier activity; FAD binding

Biological Process: branched chain family amino acid catabolic process; fatty acid beta-oxidation using acyl-CoA dehydrogenase; lipid homeostasis; lipid metabolic process

Disease: Isobutyryl-coa Dehydrogenase Deficiency
 ACAD8 ELISA Kit
 ACAD8 Recombinant
 ACAD8 Antibody
 ARC42 ELISA Kit
 ARC42 Recombinant
 ARC42 Antibody
 IBD ELISA Kit
 IBD Recombinant
 IBD Antibody
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