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Methylmalonic aciduria and homocystinuria type C protein

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Catalyzes the reductive dealkylation of cyanocobalamin to cob(II)alamin, using FAD or FMN as cofactor and NADPH as cosubstrate .

Below are the list of possible Methylmalonic aciduria and homocystinuria type C protein products. If you cannot find the target and/or product is not available in our catalog, please click here to contact us and request the product or submit your request for custom elisa kit production, custom recombinant protein production or custom antibody production. Custom ELISA Kits, Recombinant Proteins and Antibodies can be designed, manufactured and produced according to the researcher's specifications.
 

Methylmalonic aciduria and homocystinuria type C protein

 Methylmalonic aciduria and homocystinuria type C protein ELISA Kit
 Methylmalonic aciduria and homocystinuria type C protein Recombinant
 Methylmalonic aciduria and homocystinuria type C protein Antibody
Also known as Methylmalonic aciduria and homocystinuria type C protein (CblC) (Cyanocobalamin reductase (cyanide-eliminating)).
MMACHC: May be involved in the binding and intracellular trafficking of cobalamin (vitamin B12). Defects in MMACHC are the cause of methylmalonic aciduria and homocystinuria type cblC (MMAHCC). A disorder of cobalamin metabolism characterized by decreased levels of the
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coenzymes adenosylcobalamin (AdoCbl) and methylcobalamin (MeCbl). Affected individuals may have developmental, hematologic, neurologic, metabolic, ophthalmologic, and dermatologic clinical findings. Although considered a disease of infancy or childhood, some individuals develop symptoms in adulthood. Belongs to the MMACHC family.

Protein type: Motility/polarity/chemotaxis

Chromosomal Location of Human Ortholog: 1p34.1

Cellular Component: cytoplasm; cytosol

Molecular Function: cyanocobalamin reductase (cyanide-eliminating) activity; demethylase activity; glutathione binding; oxidoreductase activity; protein binding; protein homodimerization activity

Biological Process: cobalamin biosynthetic process; cobalamin metabolic process; glutathione metabolic process

Disease: Methylmalonic Aciduria And Homocystinuria, Cblc Type
 MMACHC ELISA Kit
 MMACHC Recombinant
 MMACHC Antibody
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Methylmalonic aciduria and homocystinuria type C protein homolog

 Methylmalonic aciduria and homocystinuria type C protein homolog ELISA Kit
 Methylmalonic aciduria and homocystinuria type C protein homolog Recombinant
 Methylmalonic aciduria and homocystinuria type C protein homolog Antibody
Also known as Methylmalonic aciduria and homocystinuria type C protein homolog (CblC) (Cyanocobalamin reductase (cyanide-eliminating)).
Catalyzes the reductive dealkylation of cyanocobalamin to cob(II)alamin, using FAD or FMN as cofactor and NADPH as cosubstrate. Can also catalyze the glutathione-dependent reductive demethylation of methylcobalamin, and, with much lower efficiency, the glutathi
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one-dependent reductive demethylation of adenosylcobalamin. Under anaerobic conditions cob(I)alamin is the first product; it is highly reactive and is converted to aquocob(II)alamin in the presence of oxygen. Binds cyanocobalamin, adenosylcobalamin, methylcobalamin and other, related vitamin B12 derivatives.
 MMACHC ELISA Kit
 MMACHC Recombinant
 MMACHC Antibody
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