Antibody Protein ELISA Kit from MyBioSource header Telephone 1.858.633.0165          
Fax 1.858.633.0166    Email 
menu1 Home Products Ordering Company Help menu7
   MyBioSource  rightarrow Protein Family  rightarrow N-acetylglutamate synthase  rightarrow LOG IN  rightarrow MY ACCOUNT  rightarrow CART CONTENTS  rightarrow CHECKOUT 
horiz bar
MyBioSource Menu separator
Monoclonal Antibody Monoclonal Antibody
Polyclonal Antibody Polyclonal Antibody
Secondary Antibody Secondary Antibody
Antigen Antigen
Biochemical Biochemical
cDNA Clone cDNA Clone
Peptide Peptide
Recombinant/Purified Protein Rec./Purified Protein

Custom ELISA Kit Custom ELISA Kit
Custom Protein Custom Protein
Custom Antibody Custom Antibody
Antibody Matched Pairs Antibody Matched Pairs
Antibody & Corresponding Blocking Peptide Pairs Antibody Peptide Pairs
Phospho-Specific Antibodies Phospho Antibodies
Products by Disease Products by Disease
Products by Pathway Products by Pathway
Products by Tissue Products by Tissue

arrow Advanced Search
arrow Submit Technical Q&A
arrow International Distributors
arrow Contact Us
Our Best Sellers moreseparator
 • BP-1 Recombinant Protein
 • Kappa immunoglobulin light chain (K-lgLC) ELISA Kit
 • Occludin (OCLN) ELISA Kit
 • anti-neutrophil antibody, ANA ELISA Kit
 • H5 (H5N1) (A-Egypt- chicken-2253-1-2006) Recombinant Protein
 • alpha-L-Iduronidase (IDUA) Antibody
 • Collagen Type III, Col III ELISA Kit
 • Aspartate Aminotransferase (AST or SGOT) (GPT) Assay Kit
 • 2-oxoglutae dehydrogenase, mitochondrial (OGDH) ELISA Kit
 • GIF  Antibody
 • D-3-phosphoglycerate dehydrogenase (PHGDH) Antibody
 • Suppressors Of Cytokine Signaling 3 (SOCS3) ELISA Kit
 • Deoxyribonuclease-1 (DNASE1) ELISA Kit
 • Histone H3-1 (HIST1H3C) Antibody
 downarrow more ...

N-acetylglutamate synthase

Plays a role in the regulation of ureagenesis by producing the essential cofactor N-acetylglutamate (NAG), thus modulating carbamoylphosphate synthase I (CPSI) activity.

Below are the list of possible N-acetylglutamate synthase products. If you cannot find the target and/or product is not available in our catalog, please click here to contact us and request the product or submit your request for custom elisa kit production, custom recombinant protein production or custom antibody production. Custom ELISA Kits, Recombinant Proteins and Antibodies can be designed, manufactured and produced according to the researcher's specifications.

N-acetylglutamate synthase

 N-acetylglutamate synthase ELISA Kit
 N-acetylglutamate synthase Recombinant
 N-acetylglutamate synthase Antibody
Also known as N-acetylglutamate synthase, mitochondrial (Amino-acid acetyltransferase).
NAGS: Plays a role in the regulation of ureagenesis by producing variable amounts of N-acetylglutamate (NAG), thus modulating carbamoylphosphate synthase I (CPSI) activity. Defects in NAGS are the cause of N-acetylglutamate synthase deficiency (NAGSD). NAGSD is a rare autosomal recessively inherited metaboli
c disorder leading to severe neonatal or late onset hyperammonemia without increased excretion of orotic acid. Clinical symptoms are somnolence, tachypnea, feeding difficulties, a severe neurologic presentation characterized by uncontrollable movements, developmental delay, visual impairment, failure to thrive and hyperammonemia precipitated by the introduction of high-protein diet or febrile illness. Belongs to the acetyltransferase family.

Protein type: Acetyltransferase; Amino Acid Metabolism - arginine and proline; EC; Mitochondrial

Cellular Component: mitochondrion

Molecular Function: amino-acid N-acetyltransferase activity

Biological Process: arginine biosynthetic process; glutamate metabolic process
 Nags ELISA Kit
 Nags Recombinant
 Nags Antibody
Table BarTOPTable Bar
Proteins Root Name Listing
horiz bar
 SSL   Follow us on Facebook Follow us onTwitter Follow us on Google Plus Connect us on LinkedIn Subscribe to our RSS Feed for latest products and special promotions