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Showing 1 to 50 of 101 found results for "Cystinosis"
CTNS

CTNS cDNA Clone

(#MBS1275909)

Gene Names:
CTNS; PQLC4; CTNS-LSB
Other Names:
Homo sapiens cystinosis; nephropathic; mRNA; cystinosin; lysosomal cystine transporter
  • Western Blot (WB)
  • Immunofluorescence (IF)

    CTNS Polyclonal Antibody

    (#MBS9125104)

    Gene Names:
    CTNS; PQLC4; CTNS-LSB
    Other Names:
    Cystinosin; lysosomal cystine transporter
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human
    Purification:
    Affinity Purification
    Isotype/Clone:
    Isotype: IgG
    Applications:
    Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
    cystinosis, nephropathic

    Rabbit anti-human cystinosis, nephropathic polyclonal Antibody

    (#MBS714371)

    Gene Names:
    CTNS; PQLC4; CTNS-LSB
    Other Names:
    cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human, Mouse, Rat
    Purification:
    Antigen Affinity Purified
    Isotype/Clone:
    Isotype: IgG
    Applications:
    ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC)
    Cystinosis, Nephropathic (CTNS)

    Human Cystinosis, Nephropathic (CTNS) ELISA Kit

    (#MBS9312782)

    Gene Names:
    CTNS; PQLC4; CTNS-LSB
    Other Names:
    cystinosin isoform 1; cystinosin; lysosomal cystine transporter
    Host/Reactivities:
    Reactivity: Human
    Assay Type
    Quantitative Sandwich
    Detection Range
    31.2ng/ml-1000ng/ml
    Sensitivity
    5.0ng/ml
    Cystinosin (CTNS)

    Recombinant Bovine Cystinosin (CTNS)

    (#MBS1197066)

    Gene Names:
    CTNS
    Other Names:
    Recombinant Cystinosin (CTNS); Cystinosin
    Host/Reactivities:
    Host: E Coli or Yeast or Baculovirus or Mammalian Cell
    Purity:
    Greater or equal to 85% purity as determined by SDS-PAGE.
    View Details
    Typical Testing Data/Standard Curve (for reference only)

    Human Cystinosin (CTNS) ELISA Kit

    (#MBS7250849)

    Gene Names:
    CTNS; AI195360; AW049661
    Other Names:
    cystinosin; cystinosis; nephropathic
    Host/Reactivities:
    Reactivity: Human
    Assay Type
    Quantitative Competitive
    Samples
    Serum, plasma, cell culture supernatants, body fluid and tissue homogenate
    Sensitivity
    0.1 ng/ml
    Cystinosin (CTNS)

    Recombinant Human Cystinosin (CTNS)

    (#MBS1176207)

    Gene Names:
    CTNS; Recombinant Cystinosin (CTNS); Cystinosin; PQLC4; CTNS-LSB
    Other Names:
    cystinosin isoform 1; lysosomal cystine transporter
    Host/Reactivities:
    Host: E Coli or Yeast or Baculovirus or Mammalian Cell
    Purity:
    Greater or equal to 85% purity as determined by SDS-PAGE.
    View Details
    • Testing Data
    • Western Blot (WB)
    • Western Blot (WB)
    • Western Blot (WB)
    • Western Blot (WB)
    • Western Blot (WB)

      Cystinosin (CTNS)

      (#MBS648970)

      Gene Names:
      Ctns; AI195360; AW049661
      Other Names:
      Anti -Cystinosin (CTNS); cystinosin; cystinosis; nephropathic
      Host/Reactivities:
      Host: Mouse / Reactivity: Human, Mouse, Rat
      Purification:
      Affinity PurifiedPurified by Protein A affinity chromatography.
      Isotype/Clone:
      Isotype: IgG2a,k / Clone 5G6
      Applications:
      ELISA (EL/EIA), Western Blot (WB)
      Cystinosin (CTNS)

      Canine Cystinosin (CTNS) ELISA Kit

      (#MBS7203694)

      Gene Names:
      CTNS; AI195360; AW049661
      Other Names:
      cystinosin; cystinosis; nephropathic
      Host/Reactivities:
      Reactivity: Canine
      Samples
      Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
      Cystinosin (CTNS)

      Recombinant Bovine Cystinosin (CTNS)

      (#MBS7013219)

      Gene Names:
      CTNS
      Other Names:
      cystinosin
      Host/Reactivities:
      Host: Cell Free Expression
      Purity:
      Greater or equal to 85% purity as determined by SDS-PAGE.
      CTNS

      CTNS siRNA (Human)

      (#MBS8201961)

      Gene Names:
      CTNS; PQLC4; CTNS-LSB
      Other Names:
      Cystinosin; cystinosin isoform 1; lysosomal cystine transporter
      Host/Reactivities:
      Host: Synthetic / Reactivity: Human
      Purification:
      > 97%
      Applications:
      RNA Interference (RNAi)
      Cystinosin (CTNS)

      Chicken Cystinosin (CTNS) ELISA Kit

      (#MBS7209112)

      Gene Names:
      CTNS; AI195360; AW049661
      Other Names:
      cystinosin; cystinosis; nephropathic
      Host/Reactivities:
      Reactivity: Chicken
      Samples
      Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
      • Western Blot (WB)
      • Immunofluorescence (IF)

        Anti-Cystinosin Antibody

        (#MBS8292355)

        Gene Names:
        CTNS; PQLC4; CTNS-LSB
        Other Names:
        Cystinosin; cystinosin isoform 1; lysosomal cystine transporter
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human, Mouse, Rat
        Purification:
        Purified by immunogen affinity chromatography
        Applications:
        Western Blot (WB), Immunofluorescence (IF), Immunocytochemistry (ICC)
        Cystinosin (CTNS)

        Porcine Cystinosin (CTNS) ELISA Kit

        (#MBS7249057)

        Gene Names:
        CTNS; AI195360; AW049661
        Other Names:
        cystinosin; cystinosis; nephropathic
        Host/Reactivities:
        Reactivity: Porcine
        Samples
        Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
        Cystinosin (CTNS)

        Mouse Cystinosin (CTNS) ELISA Kit

        (#MBS7218722)

        Gene Names:
        CTNS; AI195360; AW049661
        Other Names:
        cystinosin; cystinosis; nephropathic
        Host/Reactivities:
        Reactivity: Mouse
        Samples
        Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
        Cystinosin (CTNS)

        Monkey Cystinosin (CTNS) ELISA Kit

        (#MBS7222142)

        Gene Names:
        CTNS; AI195360; AW049661
        Other Names:
        cystinosin; cystinosis; nephropathic
        Host/Reactivities:
        Reactivity: Monkey
        Samples
        Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
        Cystinosin (Ctns)

        Recombinant Mouse Cystinosin (Ctns)

        (#MBS7013222)

        Gene Names:
        Ctns; AI195360; AW049661
        Other Names:
        cystinosin; cystinosis; nephropathic
        Host/Reactivities:
        Host: Cell Free Expression
        Purity:
        Greater or equal to 85% purity as determined by SDS-PAGE.
        CTNS

        CTNS siRNA (Mouse)

        (#MBS8217007)

        Gene Names:
        CTNS; AI195360; AW049661
        Other Names:
        Cystinosin; cystinosis; nephropathic
        Host/Reactivities:
        Host: Synthetic / Reactivity: Mouse
        Purification:
        > 97%
        Applications:
        RNA Interference (RNAi)
        • Western Blot (WB)
        • Western Blot (WB)

          Cystinosin (CTNS)

          (#MBS6007105)

          Gene Names:
          Ctns; AI195360; AW049661
          Other Names:
          Anti -Cystinosin (CTNS); cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Host: Rabbit / Reactivity: Human
          Purification:
          Affinity PurifiedPurified by Protein A affinity chromatography.
          Isotype/Clone:
          Isotype: IgG
          Applications:
          Western Blot (WB)
          Cystinosin (CTNS)

          Bovine Cystinosin (CTNS) ELISA Kit

          (#MBS7202571)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Bovine
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          Cystinosin (CTNS)

          Rat Cystinosin (CTNS) ELISA Kit

          (#MBS7248086)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Rat
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          Western Blot (WB)

          CTNS, CT (CTNS, Cystinosin)

          (#MBS6007321)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          Anti -CTNS; CT (CTNS; Cystinosin); cystinosin isoform 1; cystinosin; lysosomal cystine transporter
          Host/Reactivities:
          Host: Rabbit / Reactivity: Human
          Purification:
          Affinity PurifiedPurified by Protein A affinity chromatography.
          Isotype/Clone:
          Isotype: IgG
          Applications:
          ELISA (EL/EIA), Western Blot (WB)
          Western Blot (WB)

          CTNS Antibody (C-term)

          (#MBS9215258)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          Cystinosin; cystinosin isoform 1; lysosomal cystine transporter
          Host/Reactivities:
          Host: Rabbit / Reactivity: Human
          Purification:
          Peptide Affinity Purified Rabbit Polyclonal Antibody (Pab)
          Isotype/Clone:
          Isotype: Rabbit Ig
          Applications:
          Western Blot (WB), ELISA (EIA)
          Cystinosin (CTNS)

          Rabbit Cystinosin (CTNS) ELISA Kit

          (#MBS7220175)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Rabbit
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          Cystinosin (CTNS)

          Goat Cystinosin (CTNS) ELISA Kit

          (#MBS7251229)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Goat
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          Cystinosin (CTNS)

          Recombinant Human Cystinosin (CTNS)

          (#MBS7013221)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          cystinosin isoform 1; cystinosin; lysosomal cystine transporter
          Host/Reactivities:
          Host: Cell Free Expression
          Purity:
          Greater or equal to 85% purity as determined by SDS-PAGE.
          Cystinosin (CTNS)

          Sheep Cystinosin (CTNS) ELISA Kit

          (#MBS7229456)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Sheep
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          Cystinosin (CTNS)

          Guinea pig Cystinosin (CTNS) ELISA Kit

          (#MBS7229774)

          Gene Names:
          CTNS; AI195360; AW049661
          Other Names:
          cystinosin; cystinosis; nephropathic
          Host/Reactivities:
          Reactivity: Guinea Pig
          Samples
          Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate
          SDS-Page

          Recombinant Human CTNS Protein, N-His-SUMO

          (#MBS1578293)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          Cystinosin; cystinosin isoform 2; lysosomal cystine transporter
          Host/Reactivities:
          Host: E coli
          Purity:
          >90% as determined by SDS-PAGE
          Applications:
          SDS-PAGE (SDS), Western Blot (WB), ELISA (EIA), Immunogen
          Cystinosis, Nephropathic (CTNS)

          Porcine Cystinosis, Nephropathic (CTNS) ELISA Kit

          (#MBS9905596)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
          Host/Reactivities:
          Reactivity: Porcine
          Cystinosin (CTNS)

          Recombinant Human Cystinosin (CTNS), partial

          (#MBS7054535)

          Gene Names:
          CTNS; PQLC4; CTNS-LSB
          Other Names:
          cystinosin isoform 1; cystinosin; lysosomal cystine transporter
          Host/Reactivities:
          Host: E Coli or Yeast or Baculovirus or Mammalian Cell
          Purity:
          Greater or equal to 85% purity as determined by SDS-PAGE.
          View Details
          • Testing Data
          • Western Blot (WB)
          • Western Blot (WB)
          • Western Blot (WB)
          • Western Blot (WB)
          • Western Blot (WB)

            Cystinosin (CTNS) (PE)

            (#MBS6157363)

            Gene Names:
            CTNS; PQLC4; SLC66A4; CTNS-LSB
            Other Names:
            cystinosin isoform 2; cystinosin; lysosomal cystine transporter
            Host/Reactivities:
            Host: Mouse / Reactivity: Human, Mouse, Rat
            Purification:
            Purified by Protein A Affinity Chromatography.
            Isotype/Clone:
            Isotype: IgG2a,k / Clone 5G6
            Applications:
            FLISA, Western Blot (WB)
            Cystinosis, Nephropathic (CTNS)

            Cat Cystinosis, Nephropathic (CTNS) ELISA Kit

            (#MBS9905584)

            Gene Names:
            CTNS; PQLC4; CTNS-LSB
            Other Names:
            Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
            Host/Reactivities:
            Reactivity: Cat
            View Details
            Cystinosis, Nephropathic (CTNS)

            Monkey Cystinosis, Nephropathic (CTNS) ELISA Kit

            (#MBS9905593)

            Gene Names:
            CTNS; PQLC4; CTNS-LSB
            Other Names:
            Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
            Host/Reactivities:
            Reactivity: Monkey
            CTNS

            CTNS Antibody(C-term) Blocking peptide

            (#MBS9224286)

            Gene Names:
            CTNS; PQLC4; CTNS-LSB
            Other Names:
            Cystinosin; lysosomal cystine transporter
            Cystinosis, Nephropathic (CTNS)

            Canine Cystinosis, Nephropathic (CTNS) ELISA Kit

            (#MBS9905581)

            Gene Names:
            CTNS; PQLC4; CTNS-LSB
            Other Names:
            Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
            Host/Reactivities:
            Reactivity: Canine
            Cystinosis, Nephropathic (CTNS)

            Horse Cystinosis, Nephropathic (CTNS) ELISA Kit

            (#MBS9905591)

            Gene Names:
            CTNS; PQLC4; CTNS-LSB
            Other Names:
            Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
            Host/Reactivities:
            Reactivity: Horse
            • Testing Data
            • Western Blot (WB)
            • Western Blot (WB)
            • Western Blot (WB)

              Cystinosin (CTNS) (MaxLight 550)

              (#MBS6211061)

              Gene Names:
              CTNS; PQLC4; SLC66A4; CTNS-LSB
              Other Names:
              cystinosin isoform 2; cystinosin; lysosomal cystine transporter
              Host/Reactivities:
              Host: Mouse / Reactivity: Human, Mouse, Rat
              Purification:
              Purified by Protein A Affinity Chromatography.
              Isotype/Clone:
              Isotype: IgG2a,k / Clone 5G6
              Applications:
              FLISA, Western Blot (WB)
              • Testing Data
              • Western Blot (WB)
              • Western Blot (WB)
              • Western Blot (WB)
              • Western Blot (WB)
              • Western Blot (WB)

                Cystinosin (CTNS) (HRP)

                (#MBS6152060)

                Gene Names:
                CTNS; PQLC4; SLC66A4; CTNS-LSB
                Other Names:
                cystinosin isoform 2; cystinosin; lysosomal cystine transporter
                Host/Reactivities:
                Host: Mouse / Reactivity: Human, Mouse, Rat
                Purification:
                Purified by Protein A Affinity Chromatography.
                Isotype/Clone:
                Isotype: IgG2a,k / Clone 5G6
                Applications:
                ELISA (EIA), Western Blot (WB)
                Cystinosis, Nephropathic (CTNS)

                Mouse Cystinosis, Nephropathic (CTNS) ELISA Kit

                (#MBS9905594)

                Gene Names:
                CTNS; PQLC4; CTNS-LSB
                Other Names:
                Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
                Host/Reactivities:
                Reactivity: Mouse
                Cystinosis, Nephropathic (CTNS)

                Hamster Cystinosis, Nephropathic (CTNS) ELISA Kit

                (#MBS9905592)

                Gene Names:
                CTNS; PQLC4; CTNS-LSB
                Other Names:
                Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
                Host/Reactivities:
                Reactivity: Hamster
                Cystinosis, Nephropathic (CTNS)

                Rat Cystinosis, Nephropathic (CTNS) ELISA Kit

                (#MBS9905598)

                Gene Names:
                CTNS; PQLC4; CTNS-LSB
                Other Names:
                Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
                Host/Reactivities:
                Reactivity: Rat
                Cystinosin (CTNS)

                Human Cystinosin (CTNS) ELISA Kit

                (#MBS2802245)

                Gene Names:
                CTNS
                Other Names:
                CTNS-LSB; PQLC4; cystinosin
                Host/Reactivities:
                Reactivity: Human
                Assay Type
                Sandwich
                Cystinosin (Ctns)

                Recombinant Mouse Cystinosin (Ctns), partial

                (#MBS7111502)

                Gene Names:
                Ctns; AI195360; AW049661
                Other Names:
                cystinosin; cystinosis; nephropathic
                Host/Reactivities:
                Host: E Coli or Yeast or Baculovirus or Mammalian Cell
                Purity:
                Greater or equal to 85% purity as determined by SDS-PAGE.
                Western Blot (WB)

                CTNS, CT (CTNS, Cystinosin) (Biotin)

                (#MBS6289849)

                Gene Names:
                CTNS; PQLC4; CTNS-LSB
                Other Names:
                Cystinosin; cystinosin isoform 2; lysosomal cystine transporter
                Host/Reactivities:
                Host: Rabbit / Reactivity: Human
                Purification:
                Purified by Protein A and Peptide Affinity Chromatography.
                Isotype/Clone:
                Isotype: IgG
                Applications:
                Western Blot (WB), ELISA (EIA)
                • Testing Data
                • Western Blot (WB)
                • Western Blot (WB)
                • Western Blot (WB)
                • Western Blot (WB)
                • Western Blot (WB)

                  Cystinosin (CTNS) (AP)

                  (#MBS6130848)

                  Gene Names:
                  CTNS; PQLC4; SLC66A4; CTNS-LSB
                  Other Names:
                  cystinosin isoform 2; cystinosin; lysosomal cystine transporter
                  Host/Reactivities:
                  Host: Mouse / Reactivity: Human, Mouse, Rat
                  Purification:
                  Purified by Protein A Affinity Chromatography.
                  Isotype/Clone:
                  Isotype: IgG2a,k / Clone 5G6
                  Applications:
                  ELISA (EIA), Western Blot (WB)
                  Western Blot (WB)

                  Ctns Antibody - middle region

                  (#MBS3207525)

                  Gene Names:
                  CTNS; AI195360; AW049661
                  Other Names:
                  cystinosin; cystinosis; nephropathic
                  Host/Reactivities:
                  Host: Rabbit / Reactivity: Cow, Dog, Horse, Human, Mouse, Pig, Rabbit, Rat
                  Purification:
                  Affinity Purified
                  Applications:
                  Western Blot (WB)
                  • Western Blot (WB)
                  • Western Blot (WB)

                    Cystinosin (CTNS) (MaxLight 650)

                    (#MBS6375608)

                    Gene Names:
                    CTNS; PQLC4; CTNS-LSB
                    Other Names:
                    Cystinosis; nephropathic; cystinosin; lysosomal cystine transporter
                    Host/Reactivities:
                    Host: Rabbit / Reactivity: Human
                    Purification:
                    Purified by Protein A Affinity Chromatography.
                    Isotype/Clone:
                    Isotype: IgG
                    Applications:
                    Western Blot (WB)
                    • Western Blot (WB)
                    • Immunofluorescence (IF)

                      Rabbit anti-Cystinosin Antibody

                      (#MBS4510621)

                      Gene Names:
                      CTNS; PQLC4; CTNS-LSB
                      Other Names:
                      Cystinosin; cystinosin isoform 2; lysosomal cystine transporter
                      Host/Reactivities:
                      Host: Rabbit / Reactivity: Human, Mouse, Rat
                      Purification:
                      The antibody was purified by immunogen affinity chromatography.
                      Applications:
                      Western Blot (WB), Immunofluorescence (IF), Immunochemistry (IC)
                      Western Blot (WB)

                      CTNS, CT (CTNS, Cystinosin) (MaxLight 550)

                      (#MBS6289854)

                      Gene Names:
                      CTNS; PQLC4; CTNS-LSB
                      Other Names:
                      Cystinosin; cystinosin isoform 2; lysosomal cystine transporter
                      Host/Reactivities:
                      Host: Rabbit / Reactivity: Human
                      Purification:
                      Purified by Protein A and Peptide Affinity Chromatography.
                      Isotype/Clone:
                      Isotype: IgG
                      Applications:
                      Western Blot (WB), FLISA

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