Defective LMBRD1 Causes Methylmalonic Aciduria And Homocystinuria Type CblF Pathway - Page 5

Biotin--protein ligase (HLCS), ELISA Kit

Rabbit Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7218604)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Rabbit

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotin--protein ligase (HLCS), ELISA Kit

Bovine Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7228736)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Bovine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotin--protein ligase (HLCS), ELISA Kit

Rat Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7224979)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Rat

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

amnionless homolog (mouse), ELISA Kit

Rat Protein amnionless, AMN ELISA Kit

(#MBS9310959)

Gene Names:

AMN; PRO1028; amnionless

Other Names:

Rat Protein amnionless (AMN) ELISA kit; amnionless protein; visceral endoderm-specific type 1 transmembrane protein; amnionless homolog (mouse); protein amnionless; amnion associated transmembrane pro...

Host/Reactivities:

Reactivity: Rat

Biotin protein ligase (HLCS), ELISA Kit

Human Biotin protein ligase (HLCS) ELISA Kit

(#MBS7245542)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Human

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Acid Phosphatase 5, Tartrate Resistant (ACP5), Polyclonal Antibody

Biotin-Linked Antibody to Acid Phosphatase 5, Tartrate Resistant (ACP5)

(#MBS2002385)

Gene Names:

ACP5; TRAP; SPENCDI

Other Names:

Acid phosphatase 5; tartrate resistant

Host/Reactivities:

Host: Rabbit / Reactivity: Rat, Human, Mouse

Purification:

Affinity Chromatography

Applications:

Immunohistochemistry (IHC), ELISA (EIA), Western Blot (WB)

Propionyl-CoA carboxylase beta chain, mitochondrial (PCCB), Recombinant Protein

Recombinant Human Propionyl-CoA carboxylase beta chain, mitochondrial (PCCB)

(#MBS963732)

Gene Names:

PCCB

Other Names:

propionyl-CoA carboxylase beta chain; mitochondrial isoform 1; propionyl-CoA carboxylase beta subunit

Host/Reactivities:

Host: E Coli or Yeast or Baculovirus or Mammalian Cell

Purity:

Greater or equal to 85% purity as determined by SDS-PAGE.

Biotinidase (BTD), ELISA Kit

Goat Biotinidase (BTD) ELISA Kit

(#MBS7221019)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Goat

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Trypsinogen Activation Peptide, ELISA Kit

Monkey Trypsinogen Activation Peptide ELISA Kit

(#MBS024982)

Gene Names:

TAP; PRSS1; TRP1; TRY1; TRY4; TRYP1

Other Names:

Trypsin-1; protease; serine; 1 (trypsin 1)

Host/Reactivities:

Reactivity: Monkey

Assay Type

Sandwich

Ectonucleotide Pyrophosphatase/Phosphodiesterase 1 (ENPP1), Polyclonal Antibody

FITC-linked Antibody to Ectonucleotide Pyrophosphatase/Phosphodiesterase 1 (ENPP1)

(#MBS2014144)

Gene Names:

ENPP1; M6S1; NPP1; NPPS; PC-1; PCA1; ARHR2; COLED; PDNP1

Other Names:

Ectonucleotide pyrophosphatase/phosphodiesterase 1

Host/Reactivities:

Host: Rabbit / Reactivity: Rat

Purification:

Affinity Chromatography

Applications:

Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunofluorescence (IF), Western Blot (WB)

biotinidase, Polyclonal Antibody

Rabbit anti-human biotinidase polyclonal Antibody

(#MBS710636)

Gene Names:

BTD

Other Names:

biotinidase;; biotinidase

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC)

Trypsinogen Activation Peptide, ELISA Kit

Rabbit Trypsinogen Activation Peptide ELISA Kit

(#MBS025813)

Gene Names:

TAP; PRSS1; TRP1; TRY1; TRY4; TRYP1

Other Names:

Trypsin-1; protease; serine; 1 (trypsin 1)

Host/Reactivities:

Reactivity: Rabbit

Assay Type

Sandwich

View Details

Trypsinogen Activation Peptide, ELISA Kit

Camel Trypsinogen Activation Peptide ELISA Kit

(#MBS096737)

Gene Names:

TAP; PRSS1; TRP1; TRY1; TRY4; TRYP1

Other Names:

Trypsin-1; protease; serine; 1 (trypsin 1)

Host/Reactivities:

Reactivity: Camel

tartrate resistant acid phosphatase 5b (TRACP-5b), ELISA Kit

Goat tartrate resistant acid phosphatase 5b (TRACP-5b) ELISA Kit

(#MBS269604)

Gene Names:

TRACP-5b; ACP5; TRAP; SPENCDI

Other Names:

tartrate-resistant acid phosphatase type 5; acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Goat

Biotinidase (BTD), ELISA Kit

Rabbit Biotinidase (BTD) ELISA Kit

(#MBS7209092)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Rabbit

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotin--protein ligase (HLCS), ELISA Kit

Sheep Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7203395)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Sheep

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

CYB5R3, Polyclonal Antibody

Anti-CYB5R3 Antibody

(#MBS821516)

Gene Names:

CYB5R3; B5R; DIA1

Other Names:

NADH-cytochrome b5 reductase 3; Cytochrome b5 reductase; Diaphorase-1; NADH-cytochrome b5 reductase 3 isoform 1; cytochrome b5 reductase 3

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Dog

Purification:

The antibody was purified by immunogen affinity chromatography.

Applications:

Western Blot (WB), Immunohistochemistry (IHC), Immunoprecipitation (IP)

total cholesterol (TC), ELISA Kit

Goat total cholesterol (TC) ELISA Kit

(#MBS2601715)

Gene Names:

TC; TCN2; II; TC2; TC-2; TCII; TC II; D22S676; D22S750

Other Names:

transcobalamin-2 isoform 2; transcobalamin II

Host/Reactivities:

Reactivity: Goat

solute carrier family 25 (mitochondrial carrier; Graves disease autoantigen) , member 16, ELISA Kit

Human Graves disease carrier protein, SLC25A16 ELISA Kit

(#MBS9316382)

Gene Names:

SLC25A16; GDA; GDC; ML7; hML7; HGT.1; D10S105E

Other Names:

Human Graves disease carrier protein (SLC25A16) ELISA kit; RP11-524O24.4; MGC39851; solute carrier family 25; member 16; solute carrier family 25 (mitochondrial carrier; Graves disease autoantigen); g...

Host/Reactivities:

Reactivity: Human

NFS1 nitrogen fixation 1 homolog, Polyclonal Antibody

Rabbit anti-human NFS1 nitrogen fixation 1 homolog (S. cerevisiae) polyclonal Antibody

(#MBS711115)

Gene Names:

NFS1; IscS; NIFS; HUSSY-08

Other Names:

NFS1 nitrogen fixation 1 homolog (S. cerevisiae); NFS1 cysteine desulfurase

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Phosphopantothenoylcysteine Decarboxylase, Recombinant Protein

Recombinant Human Phosphopantothenoylcysteine Decarboxylase

(#MBS144314)

Gene Names:

PPCDC; coaC; MDS018; PPC-DC

Other Names:

PPCDC Human; Phosphopantothenoylcysteine Decarboxylase Human Recombinant; FLJ14585; Phosphopantothenoylcysteine Decarboxylase; phosphopantothenoylcysteine decarboxylase isoform b

Host/Reactivities:

Host: E Coli

Purity:

Greater than 95% as determined by SDS-PAGE.

Biotin--protein ligase (HLCS), ELISA Kit

Guinea pig Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7224958)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Guinea Pig

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Glutathione S Transferase Omega 1, ELISA Kit

Rabbit Glutathione S Transferase Omega 1 ELISA Kit

(#MBS725105)

Gene Names:

GSTo1; P28; SPG-R; GSTO 1-1; GSTTLp28; HEL-S-21

Other Names:

glutathione S-transferase omega-1 isoform 3; glutathione S-transferase omega 1

Host/Reactivities:

Reactivity: Rabbit

Assay Type

Competitive

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Detection Range

0.5-10ng/mL

Sensitivity

0.1ng/mL

Biotinidase (BTD), ELISA Kit

Porcine Biotinidase (BTD) ELISA Kit

(#MBS7200265)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Porcine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3), ELISA Kit

Monkey Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3) ELISA Kit

(#MBS7221600)

Gene Names:

MOCS3; UBA4

Other Names:

adenylyltransferase and sulfurtransferase MOCS3; molybdenum cofactor synthesis 3

Host/Reactivities:

Reactivity: Monkey

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Trypsinogen Activation Peptide, ELISA Kit

Canine Trypsinogen Activation Peptide ELISA Kit

(#MBS046146)

Gene Names:

TAP; PRSS1; TRP1; TRY1; TRY4; TRYP1

Other Names:

Trypsin-1; protease; serine; 1 (trypsin 1)

Host/Reactivities:

Reactivity: Canine

Assay Type

Sandwich

Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3), ELISA Kit

Mouse Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3) ELISA Kit

(#MBS7227167)

Gene Names:

MOCS3; UBA4

Other Names:

adenylyltransferase and sulfurtransferase MOCS3; molybdenum cofactor synthesis 3

Host/Reactivities:

Reactivity: Mouse

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotinidase (BTD), ELISA Kit

Chicken Biotinidase (BTD) ELISA Kit

(#MBS7238382)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Chicken

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotin--protein ligase (HLCS), ELISA Kit

Porcine Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7228652)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Porcine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

LMBRD1, Blocking Peptide

LMBRD1 Peptide

(#MBS153047)

Gene Names:

LMBRD1; NESI; LMBD1; MAHCF; C6orf209

Other Names:

BM-021; CD001; MSTP044; Probable lysosomal cobalamin transporter; HDAg-L-interacting protein NESI; LMBR1 domain containing 1

Applications:

Blocking (BL)

molybdenum cofactor synthesis 2, Polyclonal Antibody

Rabbit anti-human molybdenum cofactor synthesis 2 polyclonal Antibody

(#MBS713740)

Gene Names:

MOCS2; MPTS; MCBPE; MOCO1; MOCODB

Other Names:

molybdenum cofactor synthesis 2; MOCS2A; MOCS2B

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

Trypsinogen Activation Peptide, ELISA Kit

Bovine Trypsinogen Activation Peptide ELISA Kit

(#MBS016688)

Gene Names:

TAP; PRSS1; TRP1; TRY1; TRY4; TRYP1

Other Names:

Trypsin-1; protease; serine; 1 (trypsin 1)

Host/Reactivities:

Reactivity: Bovine

Assay Type

Sandwich

Biotinidase (BTD), ELISA Kit

Monkey Biotinidase (BTD) ELISA Kit

(#MBS7215764)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Monkey

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

PBEF1, Antibody

PBEF1 Antibody

(#MBS850071)

Gene Names:

PBEF1; NAMPT; VF; PBEF; VISFATIN; 1110035O14Rik

Other Names:

nicotinamide phosphoribosyltransferase

Host/Reactivities:

Host: Mouse / Reactivity: Human

Isotype/Clone:

Isotype: IgG1 / Clone 1D3A12

Applications:

Western Blot (WB), ELISA (EIA)

glutathione S-transferase omega 2, Polyclonal Antibody

Rabbit anti-human glutathione S-transferase omega 2 polyclonal Antibody

(#MBS719056)

Gene Names:

GSTO2; GSTO 2-2; bA127L20.1

Other Names:

glutathione S-transferase omega 2

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

Tartrate Resistant Acid Phosphatase 5B, ELISA Kit

Canine Tartrate Resistant Acid Phosphatase 5B ELISA Kit

(#MBS045720)

Gene Names:

TRACP-5B; ACP5; TRAP; SPENCDI

Other Names:

tartrate-resistant acid phosphatase type 5; acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Canine

Assay Type

Quantitative Sandwich

Samples

Body fluids, tissue homogenates, secretions or feces samples

Detection Range

0.5U/L-16U/L

Sensitivity

0.1U/L.

Tartrate Resistant Acid Phosphatase 5B, ELISA Kit

Cavy Tartrate Resistant Acid Phosphatase 5B ELISA Kit

(#MBS008734)

Gene Names:

TRACP-5B; ACP5; TRAP; SPENCDI

Other Names:

tartrate-resistant acid phosphatase type 5; acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Cavy

Assay Type

Sandwich

View Details

Biotin--protein ligase (HLCS), ELISA Kit

Monkey Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7205553)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Monkey

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotin--protein ligase (HLCS), ELISA Kit

Canine Biotin--protein ligase (HLCS) ELISA Kit

(#MBS7216521)

Gene Names:

HLCS; HCS

Other Names:

biotin--protein ligase; holocarboxylase synthetase (biotin-(proprionyl-CoA-carboxylase (ATP-hydrolysing)) ligase)

Host/Reactivities:

Reactivity: Canine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

thiamine triphosphatase, Polyclonal Antibody

Rabbit anti-human thiamine triphosphatase polyclonal Antibody

(#MBS716207)

Gene Names:

THTPA; THTP; THTPASE

Other Names:

thiamine triphosphatase; MGC2652; thiamine-triphosphatase isoform 1

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)

Bifunctional coenzyme A synthase (COASY), Recombinant Protein

Recombinant Human Bifunctional coenzyme A synthase (COASY)

(#MBS1345548)

Gene Names:

COASY; NBP; DPCK; PPAT; UKR1; NBIA6; pOV-2

Other Names:

bifunctional coenzyme A synthase isoform a; Coenzyme A synthase

Host/Reactivities:

Host: E Coli or Yeast or Baculovirus or Mammalian Cell

Purity:

Greater or equal to 85% purity as determined by SDS-PAGE.

0.02 mg (Baculovirus)

$1715

0.02 mg (Mammalian-Cell)

0.1 mg (Mammalian-Cell)

0.5 mg (Mammalian-Cell)

$7635

More Sizes/Prices

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Pyridoxal Kinase, Recombinant Protein

Recombinant Human Pyridoxal Kinase

(#MBS144291)

Gene Names:

PDXK; PKH; PNK; PRED79; C21orf97; HEL-S-1a; C21orf124

Other Names:

PDXK Human; Pyridoxal Kinase Human Recombinant; Pyridoxal kinase; Pyridoxine kinase; FLJ31940; FLJ37311; MGC15873; MGC31754; MGC52346; DKFZp566A071; pyridoxal (pyridoxine; vitamin B6) kinase

Host/Reactivities:

Host: E Coli

Purity:

Greater than 90.0% as determined by SDS-PAGE.

Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3), ELISA Kit

Sheep Adenylyltransferase and sulfurtransferase MOCS3 (MOCS3) ELISA Kit

(#MBS7250390)

Gene Names:

MOCS3; UBA4

Other Names:

adenylyltransferase and sulfurtransferase MOCS3; molybdenum cofactor synthesis 3

Host/Reactivities:

Reactivity: Sheep

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Biotinidase (BTD), ELISA Kit

Canine Biotinidase (BTD) ELISA Kit

(#MBS7221614)

Gene Names:

BTD

Other Names:

biotinidase

Host/Reactivities:

Reactivity: Canine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

CYB5R3, Blocking Peptide

CYB5R3 Blocking Peptide

(#MBS822557)

Gene Names:

CYB5R3; B5R; DIA1

Other Names:

NADH-cytochrome b5 reductase 3; Cytochrome b5 reductase; Diaphorase-1; NADH-cytochrome b5 reductase 3 isoform 1; cytochrome b5 reductase 3

Host/Reactivities:

Host: Synthetic / Reactivity: Human, Dog

Purity:

>85%

Applications:

Blocking (BL)

Tartrate Resistant Acid Phosphatase 5B, ELISA Kit

Monkey Tartrate Resistant Acid Phosphatase 5B ELISA Kit

(#MBS025470)

Gene Names:

TRACP-5B; ACP5; TRAP; SPENCDI

Other Names:

tartrate-resistant acid phosphatase type 5; acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Monkey

Assay Type

Quantitative Sandwich

Samples

Porcine Serum, Plasma Or Tissue Homogenates Samples

Detection Range

0.5U/L-16U/L

Sensitivity

0.1U/L.

CD320 antigen (CD320), Recombinant Protein

Recombinant Human CD320 antigen (CD320), partial

(#MBS1486094)

Gene Names:

CD320; 8D6; 8D6A; TCBLR

Other Names:

CD320 antigen isoform 2; CD320 molecule

Host/Reactivities:

Host: E Coli or Yeast or Baculovirus or Mammalian Cell

Purity:

Greater or equal to 85% purity as determined by SDS-PAGE.

0.5 mg (E-Coli)

$1320

0.05 mg (Baculovirus)

$1320

0.5 mg (Yeast)

$1595

0.05 mg (Mammalian-Cell)

0.1 mg (Mammalian-Cell)

$2530

More Sizes/Prices

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PANK2, Blocking Peptide

PANK2 Blocking Peptide

(#MBS822875)

Gene Names:

PANK2; HSS; HARP; PKAN; NBIA1; C20orf48

Other Names:

Pantothenate kinase 2; mitochondrial; hPanK2; Pantothenic acid kinase 2; mitochondrial isoform 2

Host/Reactivities:

Host: Synthetic / Reactivity: Human, Mouse, Rat

Purity:

>85%

Applications:

Blocking (BL)

Glucose Transporter 3 (GLUT3), ELISA Kit

Rat Glucose Transporter 3 (GLUT3) ELISA Kit

(#MBS2023892)

Gene Names:

GLUT3; SLC2A3

Other Names:

Solute Carrier Family 2(Facilitated Glucose Transporter)Member 3; Glucose transporter type 3; brain; glucose transporter 3; solute carrier family 2 (facilitated glucose transporter); member 3

Host/Reactivities:

Reactivity: Rat

Assay Type

Double-antibody Sandwich

Samples

Tissue Homogenates, Cell Lysates, Cell Culture Supernates And Other Biological Fluids

Detection Range

0.156-10ng/mL

Sensitivity

0.054ng/mL

Popular

24-Strip-Wells