Lysosome Pathway - Page 16

beta-D-Glucuronide glucuronosohydrolase, Active Protein

beta-D-Glucuronide glucuronosohydrolase (r-beta-Glucuronidase)

(#MBS682157)

Gene Names:

beta-Glucuronidase; GUSB; BG; MPS7; FLJ39445

Other Names:

beta-D-Glucuronide glucuronosohydrolase; r-beta-Glucuronidase; glucuronidase; beta

300 Units

$365

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ATPase, H+ transporting, lysosomal accessory protein 1, Polyclonal Antibody

Rabbit anti-human ATPase, H+ transporting, lysosomal accessory protein 1 polyclonal Antibody

(#MBS711360)

Gene Names:

ATP6AP1; 16A; CF2; Ac45; XAP3; XAP-3; ATP6S1; VATPS1; ATP6IP1

Other Names:

ATPase; H+ transporting; lysosomal accessory protein 1; MGC129781

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

cathepsin D, ELISA Kit

Human cathepsin D ELISA Kit

(#MBS726971)

Gene Names:

Cath-D; CTSD; CPSD; CLN10

Other Names:

Human cathepsin D (Cath-D); Human cathepsin D ELISA Kit; cathepsin D; cathepsin D (Human)

Host/Reactivities:

Reactivity: Human

Assay Type

Quantitative Competitive

Samples

Serum, plasma, cell culture supernatants, body fluid and tissue homogenate

Sensitivity

1.0 ng/mL

Cathepsin C (CTSC), Recombinant Protein

Recombinant Cathepsin C (CTSC)

(#MBS2011037)

Gene Names:

CTSC; JP; HMS; JPD; PLS; CPPI; DPP1; DPPI; PALS; DPP-I; PDON1

Other Names:

dipeptidyl peptidase 1 isoform c; cathepsin C

Host/Reactivities:

Host: E.coli / Reactivity: Homo sapiens (Human)

Purity:

> 97%

Applications:

Positive Control, Immunogen, SDS-PAGE, Western Blot (WB),

Lysosomal Associated Membrane Protein 2 (LAMP2), ELISA Kit

Human Lysosomal Associated Membrane Protein 2 (LAMP2) ELISA Kit

(#MBS454201)

Gene Names:

LAMP2; LAMPB; CD107b; LAMP-2; LGP110

Other Names:

HAVCR1; TIM1; TIMD1; HAVCR; Hepatitis A Virus Cellular Receptor 1;; lysosome-associated membrane glycoprotein 2 isoform C; lysosomal associated membrane protein 2

Host/Reactivities:

Reactivity: Human

Assay Type

Quantitative Sandwich

Samples

Human serum, plasma or other biological fluids

Detection Range

62.5-4000pg/mL

Sensitivity

< 23.5pg/mL

adaptor-related protein complex 4, mu 1 subunit, Polyclonal Antibody

Rabbit anti-human adaptor-related protein complex 4, mu 1 subunit polyclonal Antibody

(#MBS713155)

Gene Names:

AP4M1; MU-4; CPSQ3; SPG50; MU-ARP2

Other Names:

adaptor-related protein complex 4; mu 1 subunit

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

aryl sulfatase A, ELISA Kit

Human aryl sulfatase A ELISA Kit

(#MBS729185)

Gene Names:

ASA; ARSA; MLD

Other Names:

arylsulfatase A isoform a; arylsulfatase A

Host/Reactivities:

Reactivity: Human

Assay Type

Quantitative Competitive or Sandwich

Samples

Serum, plasma, cell culture supernatants, body fluid and tissue homogenate

Sensitivity

0.1 ng/mL

Popular

48-Strip-Wells-(Competitive)

$580

48-Strip-Wells-(Sandwich)

$580

96-Strip-Wells-(Competitive)

$825

96-Strip-Wells-(Sandwich)

$825

5x96-Strip-Wells-(Competitive)

$3640

5x96-Strip-Wells-(Sandwich)

$3640

10x96-Strip-Wells-(Competitive)

$6865

10x96-Strip-Wells-(Sandwich)

$6865

More Sizes/Prices

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IGF2R, Antibody

IGF2R (Phospho-Ser2409) Antibody

(#MBS852983)

Gene Names:

IGF2R; MPR1; MPRI; CD222; CIMPR; M6P-R; MPR300; CI-M6PR; MPR 300; M6P/IGF2R

Other Names:

300 kDa mannose 6-phosphate receptor; CD222 antigen; CI Man-6-P receptor; CI-MPR; cation-independent mannose-6-phosphate receptor; insulin-like growth factor 2 receptor; insulin like growth factor 2 r...

Host/Reactivities:

Reactivity: Human, Mouse

Purification:

Affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific phosphopeptide. The antibody against non-phosphopeptide was removed by chromatography using non-phosphopeptide...

Applications:

Western Blot (WB), Immunohistochemistry (IHC), ELISA (EIA)

ATP-binding cassette, sub-family B (MDR/TAP), member 9, Polyclonal Antibody

Rabbit anti-human ATP-binding cassette, sub-family B (MDR/TAP), member 9 polyclonal Antibody

(#MBS711297)

Gene Names:

ABCB9; TAPL; EST122234

Other Names:

ATP-binding cassette; sub-family B (MDR/TAP); member 9; KIAA1520; isoform CRA_b

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

ABCA2, siRNA

ABCA2 siRNA (Human)

(#MBS8210257)

Gene Names:

ABCA2; ABC2

Other Names:

KIAA1062; ATP-binding cassette sub-family A member 2; ATP-binding cassette transporter 2; ATP-binding cassette 2; ATP-binding cassette sub-family A member 2 isoform a; ATP-binding cassette; sub-family...

Host/Reactivities:

Host: Synthetic / Reactivity: Human

Purification:

> 97%

Applications:

RNA Interference (RNAi)

Acid ceramidase (ASAH1), ELISA Kit

Rabbit Acid ceramidase (ASAH1) ELISA Kit

(#MBS7212541)

Gene Names:

ASAH1; AC; PHP; ASAH; PHP32; ACDase; SMAPME

Other Names:

acid ceramidase; N-acylsphingosine amidohydrolase (acid ceramidase) 1

Host/Reactivities:

Reactivity: Rabbit

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Acid Ceramidase, Polyclonal Antibody

Anti-Acid Ceramidase Antibody

(#MBS8245649)

Gene Names:

ASAH1; AC; PHP; ASAH; PHP32; ACDase; SMAPME

Other Names:

Acid ceramidase; Acid CDase; Acylsphingosine deacylase; N-acylsphingosine amidohydrolase; Putative 32 kDa heart protein; acid ceramidase isoform c; N-acylsphingosine amidohydrolase (acid ceramidase) 1

Host/Reactivities:

Reactivity: Human

Purification:

The antibody was purified by immunogen affinity chromatography.

Applications:

Western Blot (WB)

Acid Phosphatase 5, Tartrate Resistant, ELISA Kit

Camel Acid Phosphatase 5, Tartrate Resistant ELISA Kit

(#MBS091955)

Gene Names:

ACP5; TRAP; SPENCDI

Other Names:

acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Camel

Acid Sphingomyelinase (ASM), ELISA Kit

Mouse Acid Sphingomyelinase (ASM) ELISA Kit

(#MBS261759)

Gene Names:

ASM; SMPD1; NPD; ASMASE

Other Names:

acid sphingomyelinase; sphingomyelin phosphodiesterase 1; acid lysosomal

Host/Reactivities:

Reactivity: Mouse

Assay Type

Quantitative Sandwich

Samples

Mouse serum, plasma or cell culture supernatant

Detection Range

10 ng/ml-0.156 ng/ml

Sensitivity

Up to 0.05 ng/ml

N-Acetylgalactosaminidase Alpha (NAGa), Polyclonal Antibody

Biotin-Linked Antibody to N-Acetylgalactosaminidase Alpha (NAGa)

(#MBS2005773)

Gene Names:

NAGa; GALB; D22S674

Other Names:

N-acetylgalactosaminidase; alpha-; isoform CRA_a

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat, Pig

Purification:

Antigen-specific Affinity Chromatography

Applications:

Western Blot (WB); Immunohistochemistry (IHC); Immunocytochemistry (ICC); Immunofluorescence (IF).

Battenin (BTS), ELISA Kit

Human Battenin (BTS) ELISA Kit

(#MBS9300101)

Gene Names:

BTS; CLN3; JNCL

Other Names:

battenin; ceroid-lipofuscinosis; neuronal 3

Host/Reactivities:

Reactivity: Human

GC (Glucosylceramidase, GLUC, Acid beta-Glucosidase, GBA, Alglucerase, beta-Glucocerebrosidase, D-glucosyl-N-acylsphingosine Glucohydrolase, Imiglucerase), Polyclonal Antibody

GC (Glucosylceramidase, GLUC, Acid beta-Glucosidase, GBA, Alglucerase, beta-Glucocerebrosidase, D-glucosyl-N-acylsphingosine Glucohydrolase, Imiglucerase)

(#MBS6002380)

Gene Names:

GBA; GCB; GBA1; GLUC

Other Names:

Anti -GC (Glucosylceramidase; Acid beta-Glucosidase; Alglucerase; beta-Glucocerebrosidase; D-glucosyl-N-acylsphingosine Glucohydrolase; Imiglucerase); Glucosylceramidase; glucosidase; beta; acid

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse

Purification:

Affinity PurifiedPurified by immunoaffinity chromatography.

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EL/EIA), Western Blot (WB)

Acid Phosphatase 5, Tartrate Resistant, ELISA Kit

Sheep Acid Phosphatase 5, Tartrate Resistant ELISA Kit

(#MBS025253)

Gene Names:

ACP5; TRAP; SPENCDI

Other Names:

acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Sheep

Assay Type

Sandwich

Acid Sphingomyelinase, ELISA Kit

Rat Acid Sphingomyelinase ELISA Kit

(#MBS017899)

Gene Names:

ASM; SMPD1; NPD; ASMASE

Other Names:

acid sphingomyelinase; sphingomyelin phosphodiesterase 1; acid lysosomal

Host/Reactivities:

Reactivity: Rat

Assay Type

Quantitative Sandwich

Detection Range

0.625ng/ml-20ng/ml

Sensitivity

0.1ng/ml

Cathepsin C HC, Polyclonal Antibody

Anti-Cathepsin C HC Antibody

(#MBS8218852)

Gene Names:

CTSC; JP; HMS; JPD; PLS; CPPI; DPP1; DPPI; PALS; DPP-I; PDON1

Other Names:

Dipeptidyl peptidase 1; Cathepsin C; Cathepsin J; Dipeptidyl peptidase I; Dipeptidyl transferase; dipeptidyl peptidase 1 isoform c

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat, Bovine, Dog

Purification:

The antibody was purified by immunogen affinity chromatography.

Applications:

Western Blot (WB)

Cystinosis, Nephropathic (CTNS), ELISA Kit

Human Cystinosis, Nephropathic (CTNS) ELISA Kit

(#MBS9312782)

Gene Names:

CTNS; PQLC4; CTNS-LSB

Other Names:

cystinosin isoform 1; cystinosin; lysosomal cystine transporter

Host/Reactivities:

Reactivity: Human

Assay Type

Quantitative Sandwich

Detection Range

31.2ng/ml-1000ng/ml

Sensitivity

5.0ng/ml

N-Acetylgalactosaminidase Alpha, ELISA Kit

Bovine N-Acetylgalactosaminidase Alpha ELISA Kit

(#MBS092718)

Gene Names:

NAGalpha; NAGA; GALB; D22S674

Other Names:

N-acetylgalactosaminidase; alpha-; isoform CRA_a

Host/Reactivities:

Reactivity: Bovine

Cathepsin G, ELISA Kit

Human Cathepsin G ELISA Kit

(#MBS763326)

Gene Names:

CTSG; CG; CATG

Other Names:

CTSG (Cathepsin G)/CG/CATG; cathepsin G preproprotein; cathepsin G

Host/Reactivities:

Reactivity: Human

Assay Type

Sandwich

Samples

Serum, plasma, cell culture supernatant and other biological samples

Detection Range

0.156-10ng/ml

Sensitivity

0.094ng/ml

CD68, Monoclonal Antibody

MOUSE ANTI HUMAN CD68

(#MBS214080)

Gene Names:

CD68; GP110; LAMP4; SCARD1

Other Names:

macrosialin isoform B; CD68 molecule

Host/Reactivities:

Host: Mouse

Isotype/Clone:

Isotype: IgG2a / Clone 514H12

Applications:

Immunohistology Frozen, Immunofluorescence (IF), Immunohistology Paraffin*

alpha-Galactosidase, ELISA Kit

Canine alpha-Galactosidase ELISA Kit

(#MBS742665)

Gene Names:

alphaGAL; GLA; aGAL; GALA

Other Names:

Canine a-Galactosidase ELISA Kit; alpha-galactosidase; partial; galactosidase; alpha

Host/Reactivities:

Reactivity: Canine

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

adaptor-related protein complex 3, mu 1 subunit, ELISA Kit

Human AP-3 complex subunit mu-1, AP3M1 ELISA Kit

(#MBS9320550)

Gene Names:

AP3M1

Other Names:

Human AP-3 complex subunit mu-1 (AP3M1) ELISA kit; MGC22164; AP-3 adapter complex mu3A subunit; OTTHUMP00000019860; clathrin adaptor complex AP3; mu-3A subunit; mu-adaptin 3A; adaptor-related protein ...

Host/Reactivities:

Reactivity: Human

N-acetylgalactosamine-6-sulfatase, Polyclonal Antibody

Rabbit anti-human N-acetylgalactosamine-6-sulfatase polyclonal Antibody, FITC

(#MBS1491463)

Gene Names:

GALNS; GAS; MPS4A; GalN6S; GALNAC6S

Other Names:

Chondroitinsulfatase Galactose-6-sulfate sulfatase N-acetylgalactosamine-6-sulfate sulfatase; N-acetylgalactosamine-6-sulfatase; galactosamine (N-acetyl)-6-sulfatase

Host/Reactivities:

Host: Rabbit / Reactivity: Human

Purification:

Caprylic Acid Ammonium Sulfate Precipitation Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA)

Iduronate 2-Sulfatase, Polyclonal Antibody

Iduronate 2-Sulfatase (IDS, MPS2, SIDS)

(#MBS622047)

Gene Names:

IDS; MPS2; SIDS

Other Names:

Anti -Iduronate 2-Sulfatase (IDS; SIDS); iduronate 2-sulfatase

Host/Reactivities:

Host: Goat / Reactivity: Human

Purification:

Affinity PurifiedPurified by affinity chromatography.

Applications:

ELISA (EL/EIA), Western Blot (WB)

Cathepsin H, Polyclonal Antibody

Cathepsin H antibody

(#MBS534520)

Gene Names:

CTSH; ACC4; ACC5; CPSB; ACC-4; ACC-5; minichain

Other Names:

Polyclonal Cathepsin H; Anti-Cathepsin H; cathepsin H; partial

Host/Reactivities:

Host: Rabbit / Reactivity: Human

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

Cathepsin H, Active Protein

Cathepsin H protein

(#MBS537189)

Gene Names:

CTSH; ACC4; ACC5; CPSB; ACC-4; ACC-5; minichain

Other Names:

cathepsin H; partial

Host/Reactivities:

Host: Human

Purity:

> 80% pure

Applications:

User optimized

N (4)- (beta-N-acetylglucosaminyl)-L-asparaginase, Polyclonal Antibody

Rabbit anti-human N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase polyclonal Antibody, Biotin conjugated

(#MBS1493824)

Gene Names:

AGA; GA; AGU; ASRG

Other Names:

Aspartylglucosaminidase; Glycosylasparaginase; N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase; N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase isoform 1 preproprotein

Host/Reactivities:

Host: Rabbit / Reactivity: Human

Purification:

Caprylic Acid Ammonium Sulfate Precipitation Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA)

insulin-like growth factor 2 receptor, Polyclonal Antibody

Rabbit anti-human insulin-like growth factor 2 receptor polyclonal Antibody

(#MBS711804)

Gene Names:

IGF2R; MPR1; MPRI; CD222; CIMPR; M6P-R

Other Names:

insulin-like growth factor 2 receptor

Host/Reactivities:

Host: Rabbit / Reactivity: Human

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

Cathepsin D, Active Protein

Cathepsin D protein

(#MBS537910)

Gene Names:

CTSD; CPSD; CLN10; HEL-S-130P

Other Names:

cathepsin D; partial

Host/Reactivities:

Host: Human

Purity:

> 98% pure

Applications:

User optimized

Lipase A, Lysosomal Acid, ELISA Kit

Goose Lipase A, Lysosomal Acid ELISA Kit

(#MBS090168)

Gene Names:

LIPA; LAL; CESD

Other Names:

Lysosomal acid lipase/cholesteryl ester hydrolase; lipase A; lysosomal acid; cholesterol esterase

Host/Reactivities:

Reactivity: Goose

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Acid Phosphatase 5, Tartrate Resistant, ELISA Kit

Goat Acid Phosphatase 5, Tartrate Resistant ELISA Kit

(#MBS044680)

Gene Names:

ACP5; TRAP; SPENCDI

Other Names:

acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Goat

Assay Type

Sandwich

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N-Acetylgalactosaminidase Alpha (NAGa), Recombinant Protein

Recombinant N-Acetylgalactosaminidase Alpha (NAGa)

(#MBS2011425)

Gene Names:

NAGa; GALB; D22S674

Other Names:

alpha-N-acetylgalactosaminidase; N-acetylgalactosaminidase; alpha-

Host/Reactivities:

Host: E Coli

Purity:

> 95%

Applications:

SDS-PAGE, Western Blot (WB), ELISA (EIA), Immunoprecipitation (IP)

Niemann-Pick disease, type C1, Polyclonal Antibody

Rabbit anti-human Niemann-Pick disease, type C1 polyclonal Antibody

(#MBS712151)

Gene Names:

NPC1; NPC

Other Names:

Niemann-Pick disease; type C1

Host/Reactivities:

Host: Rabbit / Reactivity: Human, Mouse, Rat

Purification:

Antigen Affinity Purified

Isotype/Clone:

Isotype: IgG

Applications:

ELISA (EIA), Western Blot (WB)

N-acetylglucosamine-1-phosphate transferase, gamma subunit, ELISA Kit

Human N-acetylglucosamine-1-phosphotransferase subunit gamma, GNPTG ELISA Kit

(#MBS9330518)

Gene Names:

GNPTG; RJD9; GNPTAG; LP2537; C16orf27

Other Names:

Human N-acetylglucosamine-1-phosphotransferase subunit gamma (GNPTG) ELISA kit; GlcNAc-phosphotransferase gamma-subunit; N-acetylglucosamine-1-phosphotransferase; gamma subunit; N-acetylglucosamine-1-...

Host/Reactivities:

Reactivity: Human

Assay Type

Quantitative Sandwich

Samples

Undiluted original Human serum, plasma or tissue homogenates samples

Detection Range

0.625ng/ml-20ng/ml

Sensitivity

0.1ng/ml

Lipase A, Lysosomal Acid, ELISA Kit

Donkey Lipase A, Lysosomal Acid ELISA Kit

(#MBS075600)

Gene Names:

LIPA; LAL; CESD

Other Names:

Lysosomal acid lipase/cholesteryl ester hydrolase; lipase A; lysosomal acid; cholesterol esterase

Host/Reactivities:

Reactivity: Donkey

View Details

N-Acetylgalactosaminidase Alpha, ELISA Kit

Pigeon N-Acetylgalactosaminidase Alpha ELISA Kit

(#MBS088623)

Gene Names:

NAGalpha; NAGA; GALB; D22S674

Other Names:

N-acetylgalactosaminidase; alpha-; isoform CRA_a

Host/Reactivities:

Reactivity: Pigeon

View Details

Acid Phosphatase 5, Tartrate Resistant, ELISA Kit

Cat Acid Phosphatase 5, Tartrate Resistant ELISA Kit

(#MBS073736)

Gene Names:

ACP5; TRAP; SPENCDI

Other Names:

acid phosphatase 5; tartrate resistant

Host/Reactivities:

Reactivity: Cat

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Cathepsin A 32k, Polyclonal Antibody

Anti-Cathepsin A 32k Antibody

(#MBS820402)

Gene Names:

CTSA; GSL; GLB2; NGBE; PPCA; PPGB

Other Names:

Lysosomal protective protein; Carboxypeptidase C; Carboxypeptidase L; Cathepsin A; Protective protein cathepsin A; Protective protein for beta-galactosidase; lysosomal protective protein isoform a

Host/Reactivities:

Reactivity: Human, Mouse, Rat

Purification:

The antibody was purified by immunogen affinity chromatography.

Applications:

Western Blot (WB)

alpha-Galactosidase, ELISA Kit

Monkey alpha-Galactosidase ELISA Kit

(#MBS740336)

Gene Names:

alphaGAL; GLA; aGAL; GALA

Other Names:

Monkey a-Galactosidase ELISA Kit; alpha-galactosidase; partial; galactosidase; alpha

Host/Reactivities:

Reactivity: Monkey

Assay Type

Competitive

Samples

Serum, plasma, Cell Culture Supernatants, body fluid and tissue homogenate

Sensitivity

0.1 ng/mL.

Lipase A, Lysosomal Acid, ELISA Kit

Pigeon Lipase A, Lysosomal Acid ELISA Kit

(#MBS067727)

Gene Names:

LIPA; LAL; CESD

Other Names:

Lysosomal acid lipase/cholesteryl ester hydrolase; lipase A; lysosomal acid; cholesterol esterase

Host/Reactivities:

Reactivity: Pigeon

View Details

adaptor-related protein complex 4, epsilon 1 subunit, ELISA Kit

Human AP-4 complex subunit epsilon-1, AP4E1 ELISA Kit

(#MBS9332068)

Gene Names:

AP4E1; CPSQ4; SPG51

Other Names:

Human AP-4 complex subunit epsilon-1 (AP4E1) ELISA kit; DKFZp686L12167; AP-4-EPSILON; adaptor-related protein complex AP-4 epsilon; adaptor-related protein complex 4; epsilon 1 subunit; AP-4 complex s...

Host/Reactivities:

Reactivity: Human