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Search results for Ataxia

Some information contained on this search result page may not be up-to-date. Please refer to the individual product pages for latest product details.

Showing 1 to 50 of 1841 found results for "ataxia"
Western Blot (WB)

FH Rabbit pAb

(#MBS9145227)

Gene Names:
FH; KCNA1; EA1; MK1; AEMK; HBK1; HUK1; MBK1; RBK1; KV1.1
Other Names:
FMRD; HLRCC; LRCC; MCL; MCUL1; fumarate hydratase; potassium voltage-gated channel subfamily A member 1; potassium voltage-gated channel; shaker-related subfamily; member 1 (episodic ataxia with myoky...
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Affinity purification
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB)
Western Blot (WB)

Anti-ATM (pS1987) Phospho Antibody

(#MBS820251)

Gene Names:
ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
Other Names:
Serine-protein kinase ATM; Ataxia telangiectasia mutated; A-T mutated; ATM serine/threonine kinase
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse, Rat
Purification:
The antibody was purified by immunogen affinity chromatography.
Applications:
Western Blot (WB)
Typical Testing Data/Standard Curve (for reference only)

Mouse ATM (Ataxia Telangiectasia Mutated) ELISA Kit

(#MBS2501227)

Gene Names:
ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
Other Names:
ATM serine/threonine kinase
Host/Reactivities:
Reactivity: Mouse
Assay Type
Sandwich
Samples
Serum, Plasma, Biological Fluids
Detection Range
7.813-500pg/mL
Sensitivity
Min: 4.688pg/mL; Max: 500pg/mL
  • Testing Data
  • Western Blot (WB)
  • Immunofluorescence (IF)

    ATM antibody

    (#MBS5309729)

    Gene Names:
    ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
    Other Names:
    Rabbit polyclonal ATM antibody; Polyclonal ATM antibody; Anti-ATM antibody; ATE antibody; TEL1 antibody; ATA antibody; ATC antibody; Ataxia telangiectasia mutated antibody; DKFZp781A0353 antibody; TEL...
    Host/Reactivities:
    Host: Rabbit
    Purification:
    Purified by immunoaffinity chromatography.
    Applications:
    Immunofluorescence (IF), Western Blot (WB)
    Typical Testing Data/Standard Curve (for reference only)

    Rat ATM (Ataxia Telangiectasia Mutated) ELISA Kit

    (#MBS2508011)

    Gene Names:
    ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
    Other Names:
    ATM serine/threonine kinase
    Host/Reactivities:
    Reactivity: Rat
    Assay Type
    Sandwich
    Samples
    Serum, Plasma, Biological Fluids
    Detection Range
    0.156-10ng/mL
    Sensitivity
    Min: 0.094ng/mL; Max: 10ng/mL
    SDS-Page

    Frataxin, 42-210aa, Human, His tag, E Coli

    (#MBS203654)

    Gene Names:
    FXN; FA; X25; CyaY; FARR; FRDA
    Other Names:
    Friedreich ataxia protein.; frataxin; mitochondrial isoform 1 preproprotein
    Host/Reactivities:
    Host: E Coli
    Purity:
    > 95% by SDS-PAGE
    Applications:
    SDS-PAGE
    Typical Testing Data/Standard Curve (for reference only)

    Human ATM (Ataxia Telangiectasia Mutated) ELISA Kit

    (#MBS2503815)

    Gene Names:
    ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
    Other Names:
    ATM serine/threonine kinase
    Host/Reactivities:
    Reactivity: Human
    Assay Type
    Sandwich
    Samples
    Serum, Plasma, Biological Fluids
    Detection Range
    0.156-10ng/mL
    Sensitivity
    Min: 0.094ng/mL; Max: 10ng/mL
    Typical Testing Data/Standard Curve (for reference only)

    Human FXN (Frataxin) ELISA Kit

    (#MBS2515805)

    Gene Names:
    FXN; FA; X25; CyaY; FARR; FRDA
    Other Names:
    frataxin; mitochondrial isoform 3 preproprotein
    Host/Reactivities:
    Reactivity: Human
    Assay Type
    Quantitative Sandwich
    Samples
    Serum, plasma and other biological fluids
    Detection Range
    23.44-1500pg/mL
    Sensitivity
    14.06pg/mL
    • Immunohistochemistry (IHC)
    • Immunohistochemistry (IHC)
    • SDS-Page
    • Testing Data

      Frataxin (Marker of Friedreich Ataxia)

      (#MBS4380564)

      Gene Names:
      FXN; FA; X25; CyaY; FARR; FRDA
      Other Names:
      d-FXN; Frataxin mature form; Frataxin (81-210); Friedreich ataxia protein; i-FXN; m56-FXN; m78-FXN; m81-FXN; frataxin; mitochondrial isoform 1 preproprotein
      Host/Reactivities:
      Host: Mouse / Reactivity: Human. Others not known.
      Purification:
      Purified Ab with BSA and Azide at 200ug/ml OR Purified Ab WITHOUT BSA and Azide at 1.0mg/ml
      Isotype/Clone:
      Isotype: IgG2b, kappa / Clone FXN/2124
      Applications:
      Immunohistology (Formalin-Fixed)
      Western Blot (WB)

      Atm Polyclonal Antibody

      (#MBS2535445)

      Gene Names:
      Atm; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
      Other Names:
      Serine-protein kinase ATM; Ataxia telangiectasia mutated; A-T mutated ; ATM serine/threonine kinase
      Host/Reactivities:
      Host: Rabbit / Reactivity: Human, Mouse
      Purification:
      Affinity purification
      Isotype/Clone:
      Isotype: IgG
      Applications:
      Western Blot (WB), Immunohistochemistry-Paraffin (IHC-p), ELISA
      Ataxia Telangiectasia Mutated

      Porcine Ataxia Telangiectasia Mutated ELISA Kit

      (#MBS037213)

      Gene Names:
      ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
      Other Names:
      Ataxia telangiectasia mutated
      Host/Reactivities:
      Reactivity: Porcine
      Assay Type
      Sandwich
      Samples
      Serum, Plasma, Tissue Homogenate, Feces and Urine
      Detection Range
      31.2 pg/ml - 1000 pg/ml.
      Sensitivity
      5.0 pg/ml.
      • Western Blot (WB)
      • Immunohistochemistry (IHC)

        Phospho-ATR(Ser428) Antibody

        (#MBS9608121)

        Gene Names:
        ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
        Other Names:
        Ataxia telangiectasia and Rad3 related; Ataxia telangiectasia and Rad3-related protein; ATR_HUMAN; FRAP Related Protein 1; FRAP-related protein 1; MEC1 mitosis entry checkpoint 1 homolog; Protein kina...
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human, Mouse, Rat
        Purification:
        Peptide affinity purification
        Isotype/Clone:
        Isotype: IgG
        Applications:
        Western Blot (WB), Immunohistochemistry (IHC)
        • Western Blot (WB)
        • Immunohistochemistry (IHC)
        • Immunohistochemistry (IHC)

          Polyclonal Antibody to Ataxia Telangiectasia Mutated (ATM)

          (#MBS2028176)

          Gene Names:
          ATM; AI256621; C030026E19Rik
          Other Names:
          serine-protein kinase ATM; ataxia telangiectasia mutated
          Host/Reactivities:
          Host: Rabbit / Reactivity: Mouse, Rat
          Purification:
          Affinity Chromatography
          Applications:
          Western Blot (WB), Immunocytochemistry (ICC), Immunohistochemistry (IHC) Formalin/Paraffin, ELISA (EIA)
          • Western Blot (WB)
          • Immunohistochemistry (IHC)

            ATR Antibody

            (#MBS9608120)

            Gene Names:
            ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
            Other Names:
            Ataxia telangiectasia and Rad3 related; Ataxia telangiectasia and Rad3-related protein; ATR_HUMAN; FRAP Related Protein 1; FRAP-related protein 1; MEC1 mitosis entry checkpoint 1 homolog; Protein kina...
            Host/Reactivities:
            Host: Rabbit / Reactivity: Human
            Purification:
            The antiserum was purified by peptide affinity chromatography using SulfoLink Coupling Resin.
            Isotype/Clone:
            Isotype: IgG
            Applications:
            Western Blot (WB), Immunohistochemistry (IHC), ELISA (EIA)
            • Western Blot (WB)
            • Immunohistochemistry (IHC)
            • Flow Cytometry (FC/FACS)
            • Flow Cytometry (FC/FACS)
            • Immunofluorescence (IF)

              Anti-Ataxin 3 Antibody

              (#MBS178269)

              Gene Names:
              ATXN3; AT3; JOS; MJD; ATX3; MJD1; SCA3
              Other Names:
              Ataxin-3; Ataxin 3; ATX3_HUMAN; EC 3.4.22.; Josephin; Machado Joseph disease (spinocerebellar ataxia 3; olivopontocerebellar ataxia 3; autosomal dominant; ataxin 3); Machado Joseph disease; Machado Jo...
              Host/Reactivities:
              Reactivity: Human, Rat
              Purification:
              Immunogen Affinity Purified
              Applications:
              Western Blot (WB), Immunohistochemistry (IHC) Paraffin/Frozen, Immunocytochemistry (ICC), Flow Cytometry (FC)
              Immunohistochemistry (IHC)

              ATR Antibody

              (#MBS7046132)

              Gene Names:
              ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
              Other Names:
              Serine/threonine-protein kinase ATR; Ataxia telangiectasia and Rad3-related protein; FRAP-related protein 1; ATR serine/threonine kinase
              Host/Reactivities:
              Host: Rabbit / Reactivity: Human
              Purification:
              >95%, Protein G purified
              Isotype/Clone:
              Isotype: IgG
              Applications:
              ELISA (EIA), Immunohistochemistry (IHC)
              • Western Blot (WB)
              • Immunofluorescence (IF)
              • Immunofluorescence (IF)
              • Immunofluorescence (IF)

                Phospho-ATM-S1981 Polyclonal Antibody

                (#MBS125807)

                Gene Names:
                ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                Other Names:
                Phospho-ATM-S1981: AT1; Serine-protein kinase ATM; ATM serine/threonine kinase
                Host/Reactivities:
                Host: Rabbit / Reactivity: Human
                Purification:
                Affinity Purification
                Isotype/Clone:
                Isotype: IgG
                Applications:
                Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
                Western Blot (WB)

                ATR Polyclonal Antibody

                (#MBS9127165)

                Gene Names:
                ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
                Other Names:
                Serine/threonine-protein kinase ATR; ATR serine/threonine kinase
                Host/Reactivities:
                Host: Rabbit / Reactivity: Human, Mouse, Rat
                Purification:
                Affinity Purification
                Isotype/Clone:
                Isotype: IgG
                Applications:
                Western Blot (WB)
                ATM

                Mouse anti ATM [11G12]: Fluorescein

                (#MBS375312)

                Gene Names:
                ATM
                Other Names:
                A-T mutated; AT mutated; AT1; ATA; Ataxia telangiectasia mutated; ataxia telangiectasia mutated (includes complementation groups A; C and D); ATC; ATD; ATDC; ATE; DKFZp781A0353; human phosphatidylinos...
                Host/Reactivities:
                Host: Mouse / Reactivity: Human
                Purification:
                Purified on protein A from tissue culture supernatant.
                Isotype/Clone:
                Isotype: IgG1 / Clone 11G12
                Applications:
                Flow Cytometry (FC/FACS), Immunocytochemistry (ICC), Immunofluorescence (IF)
                • Western Blot (WB)
                • Immunohistochemistry (IHC)
                • Immunofluorescence (IF)

                  Anti-Frataxin Antibody

                  (#MBS8245785)

                  Gene Names:
                  FXN; FA; X25; CyaY; FARR; FRDA
                  Other Names:
                  Frataxin; mitochondrial; Friedreich ataxia protein; mitochondrial isoform 1 preproprotein
                  Host/Reactivities:
                  Host: Rabbit / Reactivity: Human, Mouse, Rat
                  Purification:
                  The antibody was purified by immunogen affinity chromatography.
                  Applications:
                  Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF), Immunocytochemistry (ICC)
                  Immunofluorescence (IF)

                  ATM Polyclonal Antibody

                  (#MBS9140401)

                  Gene Names:
                  ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                  Other Names:
                  serine-protein kinase ATM; Ataxia telangiectasia mutated; ATM serine/threonine kinase
                  Host/Reactivities:
                  Host: Rabbit / Reactivity: Human, Rat
                  Purification:
                  Affinity Purification
                  Isotype/Clone:
                  Isotype: IgG
                  Applications:
                  Immunofluorescence (IF)
                  Western Blot (WB)

                  Mouse Monoclonal ATM antibody

                  (#MBS5305207)

                  Gene Names:
                  ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                  Other Names:
                  ATM antibody; ATM serine/threonine kinase
                  Host/Reactivities:
                  Host: Mouse
                  Isotype/Clone:
                  Isotype: IgG / Clone M82268
                  Applications:
                  Western Blot (WB), ELISA (EIA)
                  • Western Blot (WB)
                  • Immunohistochemistry (IHC)
                  • Immunofluorescence (IF)

                    ATM Antibody

                    (#MBS150319)

                    Gene Names:
                    ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                    Other Names:
                    Serine-protein kinase ATM; Ataxia telangiectasia mutated; A-T mutated; ATM serine/threonine kinase
                    Host/Reactivities:
                    Host: Rabbit / Reactivity: Human
                    Purification:
                    ATM Antibody is affinity chromatography purified via peptide column.
                    Isotype/Clone:
                    Isotype: IgG
                    Applications:
                    ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
                    • Western Blot (WB)
                    • Testing Data

                      ATM Antibody

                      (#MBS850513)

                      Gene Names:
                      ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                      Other Names:
                      MGC74674; DKFZp781A0353; serine-protein kinase ATM isoform a; ATM serine/threonine kinase
                      Host/Reactivities:
                      Host: Mouse / Reactivity: Human
                      Isotype/Clone:
                      Isotype: IgG1 / Clone 5C5
                      Applications:
                      Western Blot (WB), ELISA (EIA)
                      • Western Blot (WB)
                      • Immunohistochemistry (IHC)
                      • Immunohistochemistry (IHC)
                      • Immunofluorescence (IF)

                        FXN Antibody

                        (#MBS2523335)

                        Gene Names:
                        FXN; FA; X25; CyaY; FARR; FRDA
                        Other Names:
                        MGC57199; frataxin; mitochondrial isoform 3 preproprotein
                        Host/Reactivities:
                        Host: Rabbit / Reactivity: Human, Mouse, Rat
                        Purification:
                        Antigen affinity purification
                        Isotype/Clone:
                        Isotype: IgG
                        Applications:
                        Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
                        • Western Blot (WB)
                        • Western Blot (WB)

                          [KO Validated] FXN/Frataxin Polyclonal Antibody

                          (#MBS9140966)

                          Gene Names:
                          FXN; FA; X25; CyaY; FARR; FRDA
                          Other Names:
                          [KO Validated] FXN Polyclonal Antibody; frataxin; mitochondrial
                          Host/Reactivities:
                          Host: Rabbit / Reactivity: Human, Mouse
                          Purification:
                          Affinity Purification
                          Isotype/Clone:
                          Isotype: IgG
                          Applications:
                          Western Blot (WB)
                          • Western Blot (WB)
                          • Western Blot (WB)
                          • Immunohistochemistry (IHC)

                            FXN Antibody (C-term)

                            (#MBS9215230)

                            Gene Names:
                            FXN; FA; X25; CyaY; FARR; FRDA
                            Other Names:
                            Frataxin; mitochondrial; Friedreich ataxia protein; Frataxin intermediate form; i-FXN; Frataxin(56-210); m56-FXN; Frataxin(78-210); d-FXN; m78-FXN; Frataxin mature form; Frataxin(81-210); m81-FXN; mit...
                            Host/Reactivities:
                            Host: Rabbit / Reactivity: Human (Predicted Reactivity: Mouse)
                            Purification:
                            Purified Rabbit Polyclonal Antibody (Pab)
                            Isotype/Clone:
                            Isotype: Rabbit Ig
                            Applications:
                            Western Blot (WB), ELISA (EIA), Immunohistochemistry-paraffin (IHC-p)
                            Western Blot (WB)

                            Polyclonal Antibody to Ataxia Telangiectasia And Rad3 Related Protein (ATR)

                            (#MBS2028498)

                            Gene Names:
                            ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
                            Other Names:
                            serine/threonine-protein kinase ATR isoform 1; ATR serine/threonine kinase
                            Host/Reactivities:
                            Host: Rabbit / Reactivity: Homo sapiens (Human)
                            Purification:
                            Antigen-specific affinity chromatography followed by Protein A affinity chromatography
                            Applications:
                            Western Blot (WB)
                            Typical Testing Data/Standard Curve (for reference only)

                            Mouse Frataxin (FXN) ELISA Kit

                            (#MBS2023253)

                            Gene Names:
                            FXN; FH; ATFH; F4C21.17; F4C21_17; frataxin homolog
                            Other Names:
                            FA; CyaY; FARR; FRDA; X25; Friedreich ataxia protein; Frataxin intermediate form; Frataxin; mitochondrial
                            Host/Reactivities:
                            Reactivity: Mouse
                            Assay Type
                            Double-antibody Sandwich
                            Samples
                            Tissue homogenates, Cell lysates, Cell culture supernates and other biological fluids
                            Detection Range
                            0.156-10ng/mL
                            Sensitivity
                            0.054ng/mL
                            • Western Blot (WB)
                            • Immunohistochemistry (IHC)

                              ATR Antibody

                              (#MBS9604145)

                              Gene Names:
                              ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
                              Other Names:
                              Ataxia telangiectasia and Rad3 related; Ataxia telangiectasia and Rad3-related protein; ATR_HUMAN; FRAP Related Protein 1; FRAP-related protein 1; MEC1 mitosis entry checkpoint 1 homolog; Protein kina...
                              Host/Reactivities:
                              Host: Rabbit / Reactivity: Human
                              Purification:
                              The antiserum was purified by peptide affinity chromatography using SulfoLink Coupling Resin.
                              Isotype/Clone:
                              Isotype: IgG
                              Applications:
                              Western Blot (WB), Immunohistochemistry (IHC), ELISA (EIA)
                              • Western Blot (WB)
                              • Immunohistochemistry (IHC)

                                FXN Antibody

                                (#MBS9607246)

                                Gene Names:
                                FXN; FA; X25; CyaY; FARR; FRDA
                                Other Names:
                                d-FXN; Frataxin mature form; Frataxin(81-210); FRDA_HUMAN; Friedreich ataxia protein; i-FXN; m56-FXN; m78-FXN; m81-FXN; MGC57199; frataxin; mitochondrial isoform 1 preproprotein
                                Host/Reactivities:
                                Host: Rabbit / Reactivity: Human, Mouse, Rat
                                Purification:
                                The antiserum was purified by peptide affinity chromatography using SulfoLink Coupling Resin.
                                Isotype/Clone:
                                Isotype: IgG
                                Applications:
                                Western Blot (WB), Immunohistochemistry (IHC), ELISA (EIA)
                                • Western Blot (WB)
                                • Immunohistochemistry (IHC)

                                  Polyclonal Antibody to Ataxia Telangiectasia Mutated (ATM)

                                  (#MBS2026709)

                                  Gene Names:
                                  ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                                  Other Names:
                                  serine-protein kinase ATM isoform a; ATM serine/threonine kinase
                                  Host/Reactivities:
                                  Host: Rabbit / Reactivity: Human
                                  Purification:
                                  Affinity Chromatography
                                  Applications:
                                  Western Blot (WB), Immunocytochemistry (ICC), Immunohistochemistry (IHC) Formalin/Paraffin, ELISA (EIA)
                                  • Western Blot (WB)
                                  • Immunohistochemistry (IHC)
                                  • Immunohistochemistry (IHC)
                                  • Immunoprecipitation (IP)

                                    ATM Antibody

                                    (#MBS7114926)

                                    Gene Names:
                                    ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                                    Other Names:
                                    Serine-protein kinase ATM; Ataxia telangiectasia mutated; A-T mutated; serine-protein kinase ATM isoform a; ATM serine/threonine kinase
                                    Host/Reactivities:
                                    Host: Rabbit / Reactivity: Human
                                    Purification:
                                    Affinity-Chromatography
                                    Isotype/Clone:
                                    Isotype: IgG
                                    Applications:
                                    ELISA (EIA), Western Blot (WB), Immunohistochemistry (IHC), Immunoprecipitation (IP)
                                    • Western Blot (WB)
                                    • Immunohistochemistry (IHC)
                                    • Immunohistochemistry (IHC)
                                    • Immunofluorescence (IF)

                                      FXN Polyclonal Antibody

                                      (#MBS127297)

                                      Gene Names:
                                      FXN; FA; X25; CyaY; FARR; FRDA
                                      Other Names:
                                      MGC57199; Frataxin; mitochondrial
                                      Host/Reactivities:
                                      Host: Rabbit / Reactivity: Human, Mouse, Rat
                                      Purification:
                                      Affinity Purification
                                      Isotype/Clone:
                                      Isotype: IgG
                                      Applications:
                                      Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
                                      • Flow Cytometry (FC/FACS)
                                      • Western Blot (WB)
                                      • Immunohistochemistry (IHC)
                                      • Immunofluorescence (IF)

                                        FXN antibody

                                        (#MBS838690)

                                        Gene Names:
                                        FXN
                                        Other Names:
                                        Monoclonal FXN; Anti-FXN; CyaY; FA; FARR; FRDA; MGC57199; X25
                                        Host/Reactivities:
                                        Host: Mouse
                                        Purification:
                                        FXN antibody was purified by affinity chromatography.
                                        Isotype/Clone:
                                        Isotype: IgG1 / Clone 1C12
                                        Applications:
                                        Immunofluorescence (IF), Flow Cytometry (FC/FACS), Immunohistochemistry (IHC), Western Blot (WB)
                                        SDS-Page

                                        Frataxin (Mitochondrial Marker)

                                        (#MBS4380917)

                                        Gene Names:
                                        FXN; FA; X25; CyaY; FARR; FRDA
                                        Other Names:
                                        d-FXN; Frataxin mature form; Frataxin (81-210); Friedreich ataxia protein; i-FXN; m56-FXN; m78-FXN; m81-FXN; Frataxin; mitochondrial
                                        Host/Reactivities:
                                        Host: Mouse / Reactivity: Human
                                        Purification:
                                        Purified Ab with BSA and Azide at 200ug/ml OR Purified Ab WITHOUT BSA and Azide at 1.0mg/ml
                                        Isotype/Clone:
                                        Isotype: IgG1, kappa / Clone rFXN/2124
                                        Applications:
                                        ELISA (EIA)
                                        • Immunohistochemistry (IHC)
                                        • Immunohistochemistry (IHC)
                                        • Testing Data

                                          Carbonic Anhydrase VIII

                                          (#MBS4380717)

                                          Gene Names:
                                          CA8; CALS; CARP; CA-RP; CAMRQ3; CA-VIII
                                          Other Names:
                                          MGC120502; MGC99509; carbonic anhydrase-related protein isoform a; carbonic anhydrase 8
                                          Host/Reactivities:
                                          Host: Mouse / Reactivity: Human. Others not tested.
                                          Purification:
                                          Purified Ab with BSA and Azide at 200ug/ml OR Purified Ab WITHOUT BSA and Azide at 1.0mg/ml
                                          Isotype/Clone:
                                          Isotype: IgG2a / Clone CPTC-CA8-2
                                          Applications:
                                          Western Blot (WB), Immunohistology (Formalin-Fixed)
                                          • Western Blot (WB)
                                          • Immunohistochemistry (IHC)
                                          • Immunohistochemistry (IHC)
                                          • Immunofluorescence (IF)

                                            FXN Antibody

                                            (#MBS9412820)

                                            Gene Names:
                                            FXN; FA; X25; CyaY; FARR; FRDA
                                            Other Names:
                                            MGC57199; frataxin; mitochondrial isoform 1 preproprotein
                                            Host/Reactivities:
                                            Host: Rabbit / Reactivity: Human, Mouse, Rat
                                            Purification:
                                            Antibodies were purified by affinity purification using immunogen.
                                            Applications:
                                            Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
                                            Western Blot (WB)

                                            Phospho-ATR (Ser428) Antibody

                                            (#MBS9604452)

                                            Gene Names:
                                            ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
                                            Other Names:
                                            Ataxia telangiectasia and Rad3 related; Ataxia telangiectasia and Rad3-related protein; ATR_HUMAN; FRAP Related Protein 1; FRAP-related protein 1; MEC1 mitosis entry checkpoint 1 homolog; Protein kina...
                                            Host/Reactivities:
                                            Host: Rabbit / Reactivity: Human
                                            Purification:
                                            From purified rabbit serum by affinity purification via sequential chromatography on phospho-and non-phospho-peptide affinity columns.
                                            Isotype/Clone:
                                            Isotype: IgG
                                            Applications:
                                            Western Blot (WB), ELISA (EIA)
                                            SDS-Page

                                            Recombinant Human Frataxin, mitochondrial (FxN)

                                            (#MBS7110941)

                                            Gene Names:
                                            FxN; FA; X25; CyaY; FARR; FRDA
                                            Other Names:
                                            Friedreich ataxia protein; frataxin; mitochondrial isoform 1 preproprotein
                                            Host/Reactivities:
                                            Host: E Coli or Yeast or Baculovirus or Mammalian Cell
                                            Purity:
                                            Greater or equal to 85% purity as determined by SDS-PAGE.
                                            • Western Blot (WB)
                                            • Immunohistochemistry (IHC)
                                            • Immunofluorescence (IF)

                                              FXN Antibody (Center)

                                              (#MBS9205231)

                                              Gene Names:
                                              FXN; FA; X25; CyaY; FARR; FRDA
                                              Other Names:
                                              Frataxin; mitochondrial; Friedreich ataxia protein; Frataxin intermediate form; i-FXN; Frataxin(56-210); m56-FXN; Frataxin(78-210); d-FXN; m78-FXN; Frataxin mature form; Frataxin(81-210); m81-FXN; mit...
                                              Host/Reactivities:
                                              Host: Rabbit / Reactivity: Human
                                              Purification:
                                              Purified Rabbit Polyclonal Antibody (Pab)
                                              Isotype/Clone:
                                              Isotype: Rabbit Ig
                                              Applications:
                                              Western Blot (WB), ELISA (EIA), Immunohistochemistry (IHC), Immunofluorescence (IF)
                                              Western Blot (WB)

                                              ATM Polyclonal Antibody

                                              (#MBS9126187)

                                              Gene Names:
                                              ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                                              Other Names:
                                              Serine-protein kinase ATM; ATM serine/threonine kinase
                                              Host/Reactivities:
                                              Host: Rabbit / Reactivity: Human
                                              Purification:
                                              Affinity Purification
                                              Isotype/Clone:
                                              Isotype: IgG
                                              Applications:
                                              Western Blot (WB), Immunofluorescence (IF)
                                              Western Blot (WB)

                                              FXN Polyclonal Antibody

                                              (#MBS9131763)

                                              Gene Names:
                                              FXN; FA; X25; CyaY; FARR; FRDA
                                              Other Names:
                                              Frataxin; mitochondrial
                                              Host/Reactivities:
                                              Host: Rabbit / Reactivity: Human, Mouse, Rat
                                              Purification:
                                              Affinity Purification
                                              Isotype/Clone:
                                              Isotype: IgG
                                              Applications:
                                              Western Blot (WB)
                                              Western Blot (WB)

                                              ATR Polyclonal Antibody

                                              (#MBS9133961)

                                              Gene Names:
                                              ATR; FRP1; MEC1; SCKL; FCTCS; SCKL1
                                              Other Names:
                                              serine/threonine-protein kinase ATR isoform 1; ATR serine/threonine kinase
                                              Host/Reactivities:
                                              Host: Rabbit / Reactivity: Mouse
                                              Purification:
                                              Affinity Purification
                                              Isotype/Clone:
                                              Isotype: IgG
                                              Applications:
                                              Western Blot (WB)
                                              • Western Blot (WB)
                                              • Immunohistochemistry (IHC)

                                                Polyclonal Antibody to Frataxin (FXN)

                                                (#MBS2028275)

                                                Gene Names:
                                                FXN; FA; X25; CyaY; FARR; FRDA
                                                Other Names:
                                                frataxin; mitochondrial isoform 1 preproprotein
                                                Host/Reactivities:
                                                Host: Rabbit / Reactivity: Human
                                                Purification:
                                                Affinity Chromatography
                                                Applications:
                                                Western Blot (WB), Immunocytochemistry (ICC), Immunohistochemistry (IHC) Formalin/Paraffin, ELISA (EIA)
                                                SDS-Page

                                                Recombinant Ataxia Telangiectasia Mutated (ATM)

                                                (#MBS2029938)

                                                Gene Names:
                                                ATM
                                                Host/Reactivities:
                                                Host: Host: E Coli; Source: Prokaryotic expression
                                                Purity:
                                                >95%
                                                Applications:
                                                SDS-PAGE, Western Blot (WB), ELISA (EIA), Immunoprecipitation (IP)
                                                SDS-Page

                                                Recombinant Ataxia Telangiectasia And Rad3 Related Protein (ATR)

                                                (#MBS2030230)

                                                Gene Names:
                                                ATR
                                                Host/Reactivities:
                                                Host: Host: E Coli; Source: Prokaryotic expression
                                                Purity:
                                                >95%
                                                Applications:
                                                SDS-PAGE, Western Blot (WB), ELISA (EIA), Immunoprecipitation (IP)
                                                Frataxin

                                                Recombinant Human Frataxin

                                                (#MBS143636)

                                                Gene Names:
                                                FXN; FA; X25; CyaY; FARR; FRDA
                                                Other Names:
                                                Frataxin Human; Frataxin Human Recombinant; Friedreich ataxia protein; Frataxin mitochondrial; MGC57199; Frataxin; mitochondrial isoform 1 preproprotein
                                                Host/Reactivities:
                                                Host: E Coli
                                                Purity:
                                                Greater than 95.0% as determined by SDS-PAGE.
                                                Typical Testing Data/Standard Curve (for reference only)

                                                Human Ataxia Telangiectasia Mutated ELISA Kit

                                                (#MBS721915)

                                                Gene Names:
                                                ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                                                Other Names:
                                                ATM serine/threonine kinase
                                                Host/Reactivities:
                                                Reactivity: Human
                                                Assay Type
                                                Quantitative Competitive
                                                Samples
                                                Serum, plasma, cell culture supernatants, body fluid and tissue homogenate
                                                Sensitivity
                                                1.0 pg/mL
                                                Typical Testing Data/Standard Curve (for reference only)

                                                Human Ataxia Telangiectasia Mutated (ATM) ELISA Kit

                                                (#MBS2019080)

                                                Gene Names:
                                                ATM; AT1; ATA; ATC; ATD; ATE; ATDC; TEL1; TELO1
                                                Other Names:
                                                Serine-protein kinase ATM; Ataxia telangiectasia mutated; ATM serine/threonine kinase
                                                Host/Reactivities:
                                                Reactivity: Human
                                                Assay Type
                                                Double-antibody Sandwich
                                                Samples
                                                Serum, Plasma, Tissue homogenates, Cell lysates and other biological fluids
                                                Detection Range
                                                15.6-1,000pg/mL
                                                Sensitivity
                                                6.4pg/mL
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