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Showing 2051 to 2100 of 2168 found results for "Defective BTD Causes Biotidinase Deficiency Pathway"
ENPP1

ENPP1, NT (ENPP1, M6S1, NPPS, PC1, PDNP1, Ectonucleotide pyrophosphatase/phosphodiesterase family member 1, Membrane component chromosome 6 surface marker 1, Phosphodiesterase I/nucleotide pyrophosphatase 1, Plasma-cell membrane glycoprotein PC-1, Alkalin

(#MBS6295660)

Gene Names:
ENPP1; M6S1; NPP1; NPPS; PC-1; PCA1; ARHR2; COLED; PDNP1
Other Names:
PC1; Ectonucleotide pyrophosphatase/phosphodiesterase family member 1; Membrane component chromosome 6 surface marker 1; Phosphodiesterase I/nucleotide pyrophosphatase 1; Plasma-cell membrane glycopro...
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
DHFR

DHFR Polyclonal Antibody HRP Conjugated

(#MBS9464048)

Gene Names:
DHFR; DYR; DHFRP1
Other Names:
Dihydrofolate reductase
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
affinity purified by Protein A
Applications:
Western Blot (WB), Immunohistochemistry (IHC)
COASY

COASY Antibody

(#MBS9232953)

Gene Names:
COASY; NBP; DPCK; PPAT; UKR1; NBIA6; pOV-2
Other Names:
Bifunctional coenzyme A synthase; CoA synthase; Phosphopantetheine adenylyltransferase; Dephospho-CoA pyrophosphorylase; Pantetheine-phosphate adenylyltransferase; Dephospho-CoA kinase; Dephosphocoenz...
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse
Purification:
Purified Rabbit Polyclonal Antibody (Pab)
Applications:
Western Blot (WB), ELISA (EIA)
Western Blot (WB)

CD320, CT (CD320, 8D6A, CD320 antigen, 8D6 antigen, FDC-signaling molecule 8D6, Transcobalamin receptor, CD320) (MaxLight 405)

(#MBS6283087)

Gene Names:
CD320; 8D6; 8D6A; TCBLR
Other Names:
CD320 antigen; 8D6 antigen; FDC-signaling molecule 8D6; Transcobalamin receptor; CD320 antigen isoform 2; CD320 molecule
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A and Peptide Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
ACP5

ACP5, NT (ACP5, Tartrate-resistant acid phosphatase type 5, Tartrate-resistant acid ATPase, Type 5 acid phosphatase) (MaxLight 490)

(#MBS6271030)

Gene Names:
ACP5; TRAP; SPENCDI
Other Names:
Tartrate-resistant acid phosphatase type 5; Tartrate-resistant acid ATPase; Type 5 acid phosphatase; acid phosphatase 5; tartrate resistant
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
Western Blot (WB)

PNPO (Pyridoxine-5'-phosphate Oxidase, Pyridoxamine-phosphate Oxidase, FLJ10535, PDXPO) APC

(#MBS6390022)

Gene Names:
PNPO; PDXPO; HEL-S-302
Other Names:
pyridoxine-5'-phosphate oxidase; pyridoxamine 5'-phosphate oxidase
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB)
PBEF

PBEF (Pre-B cell Colony Enhancing Factor, Pre-B cell Enhancing Factor, 1110035O14Rik, DKFZP666B131, EC 2.4.2.12, MGC117256, Nicotinamide Phosphoribosyltransferase, NAmPRTase, NAMPT, Pre-B cell Colony Enhancing Factor 1, PBEF1, Visfatin) (Biotin)

(#MBS6249232)

Gene Names:
PBEF; NAMPT; VF; PBEF1; VISFATIN; 1110035O14Rik
Other Names:
Nicotinamide phosphoribosyltransferase
Host/Reactivities:
Host: Mouse / Reactivity: Human
Purification:
Purified by Protein G Affinity Chromatography
Isotype/Clone:
Isotype: IgG1 / Clone 10B2534
Applications:
ELISA (EIA), Western Blot (WB)
PBEF

PBEF (Pre-B cell Colony Enhancing Factor, Pre-B cell Enhancing Factor, 1110035O14Rik, DKFZP666B131, EC 2.4.2.12, MGC117256, Nicotinamide Phosphoribosyltransferase, NAmPRTase, NAMPT, Pre-B cell Colony Enhancing Factor 1, PBEF1, Visfatin) (MaxLight 405)

(#MBS6253131)

Gene Names:
PBEF; NAMPT; VF; PBEF1; VISFATIN; 1110035O14Rik
Other Names:
Nicotinamide phosphoribosyltransferase
Host/Reactivities:
Host: Mouse / Reactivity: Human
Purification:
Purified by Protein G Affinity Chromatography
Isotype/Clone:
Isotype: IgG1 / Clone 10B2534
Applications:
FLISA, Western Blot (WB)
ENPP1

ENPP1, NT (ENPP1, M6S1, NPPS, PC1, PDNP1, Ectonucleotide pyrophosphatase/phosphodiesterase family member 1, Membrane component chromosome 6 surface marker 1, Phosphodiesterase I/nucleotide pyrophosphatase 1, Plasma-cell membrane glycoprotein PC-1, Alkalin

(#MBS6295663)

Gene Names:
ENPP1; M6S1; NPP1; NPPS; PC-1; PCA1; ARHR2; COLED; PDNP1
Other Names:
PC1; Ectonucleotide pyrophosphatase/phosphodiesterase family member 1; Membrane component chromosome 6 surface marker 1; Phosphodiesterase I/nucleotide pyrophosphatase 1; Plasma-cell membrane glycopro...
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
Transcobalamin II, Macrocytic Anemia (TCN2)

APC-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

(#MBS2165367)

Gene Names:
TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
Other Names:
Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
Host/Reactivities:
Host: Mouse / Reactivity: Human
Purification:
Protein A + Protein G affinity chromatography
Applications:
Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
ENPP1

ENPP1 Rabbit Polyclonal Antibody

(#MBS9514391)

Gene Names:
ENPP1; M6S1; NPPS; PC1; PDNP1; NPP1; PC-1; PCA1; ARHR2; COLED
Other Names:
BH6842; Ectonucleotide pyrophosphatase/phosphodiesterase family member 1 (E-NPP 1)(Membrane component chromosome 6 surface marker 1)(Phosphodiesterase I/nucleotide pyrophosphatase 1)(Plasma-cell membr...
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse, Rat
Purification:
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Applications:
Western Blot (WB), ELISA (EIA)
Western Blot (WB)

COASY Rabbit mAb

(#MBS4761115)

Gene Names:
PPAT; COASY; NBP; DPCK; UKR1; NBIA6; pOV-2
Other Names:
CoA kinase; DPCOAK; POV2; Bifunctional coenzyme A synthase; CoA synthase
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Affinity Chromatography
Isotype/Clone:
Isotype: IgG / Clone R38-9L-7
Applications:
Western Blot (WB)
AMNLS

AMNLS Rabbit Polyclonal Antibody

(#MBS9513342)

Gene Names:
AMNLS; AMN; UNQ513/PRO1028; PRO1028; amnionless
Other Names:
BH6842; Protein amnionless; amnion associated transmembrane protein
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse
Purification:
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Applications:
Western Blot (WB), ELISA (EIA)
Pantothenate Kinase 1

Pantothenate Kinase 1, NT (Pantothenic Acid Kinase 1, PANK1, PANK1a, PANK1b, PANK, hPanK1, hPanK, MGC24596) (MaxLight 490)

(#MBS6491894)

Gene Names:
PANK1; PANK
Other Names:
EC=2.7.1.33; pantothenate kinase 1 isoform alpha; pantothenate kinase 1
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse
Purification:
Purified by Protein G Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
Western Blot (WB)

PBEF Rabbit Polyclonal Antibody

(#MBS9512675)

Gene Names:
PBEF; NAMPT; VF; PBEF1; VISFATIN; 1110035O14Rik
Other Names:
Nicotinamide phosphoribosyltransferase (NAmPRTase)(Nampt)(EC 2.4.2.12)(Pre-B-cell colony-enhancing factor 1)(Pre-B cell-enhancing factor)(Visfatin); BH6842; Nicotinamide phosphoribosyltransferase
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse, Rat
Purification:
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Applications:
Western Blot (WB), ELISA (EIA)
MCCC2

MCCC2, CT (MCCC2, MCCB, Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial, 3-methylcrotonyl-CoA carboxylase 2, 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta) (MaxLight 550)

(#MBS6319591)

Gene Names:
MCCC2; MCCB
Other Names:
Methylcrotonoyl-CoA carboxylase beta chain; mitochondrial; 3-methylcrotonyl-CoA carboxylase 2; 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligas...
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), FLISA
Western Blot (WB)

CD320, CT (CD320, 8D6A, CD320 antigen, 8D6 antigen, FDC-signaling molecule 8D6, Transcobalamin receptor, CD320) (Biotin)

(#MBS6283084)

Gene Names:
CD320; 8D6; 8D6A; TCBLR
Other Names:
CD320 antigen; 8D6 antigen; FDC-signaling molecule 8D6; Transcobalamin receptor; CD320 antigen isoform 2; CD320 molecule
Host/Reactivities:
Host: Rabbit / Reactivity: Human
Purification:
Purified by Protein A and Peptide Affinity Chromatography.
Isotype/Clone:
Isotype: IgG
Applications:
Western Blot (WB), ELISA (EIA)
Transcobalamin II, Macrocytic Anemia (TCN2)

PE-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

(#MBS2164499)

Gene Names:
TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
Other Names:
Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
Host/Reactivities:
Host: Mouse / Reactivity: Human
Purification:
Protein A + Protein G affinity chromatography
Applications:
Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
PBEF/NAMPT

Rabbit Anti Human PBEF/NAMPT Polyclonal Affinity Purified (PBS with 0.02% sodium azide, 50% glycerol, pH7.3)(Western Blot, IHC, Immunofluorescence)

(#MBS8424266)

Gene Names:
PBEF/NAMPT; NAMPT; VF; PBEF; PBEF1; VISFATIN; 1110035O14Rik
Other Names:
nicotinamide phosphoribosyltransferase
Host/Reactivities:
Host: Rabbit / Reactivity: Human, Mouse, Rat
Purification:
Affinity Purified
Applications:
Western Blot (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
PBEF

PBEF (Pre-B cell Colony Enhancing Factor, Pre-B cell Enhancing Factor, 1110035O14Rik, DKFZP666B131, EC 2.4.2.12, MGC117256, Nicotinamide Phosphoribosyltransferase, NAmPRTase, NAMPT, Pre-B cell Colony Enhancing Factor 1, PBEF1, Visfatin) (FITC)

(#MBS6250138)

Gene Names:
PBEF; NAMPT; VF; PBEF1; VISFATIN; 1110035O14Rik
Other Names:
Nicotinamide phosphoribosyltransferase
Host/Reactivities:
Host: Mouse / Reactivity: Human
Purification:
Purified by Protein G Affinity Chromatography
Isotype/Clone:
Isotype: IgG1 / Clone 10B2534
Applications:
ELISA (EIA), Western Blot (WB)
  • Flow Cytometry (FC/FACS)
  • Immunocytochemistry (ICC)
  • Immunohistochemistry (IHC)
  • Immunohistochemistry (IHC)
  • Immunoprecipitation (IP)
  • Western Blot (WB)

    Rabbit anti-NAMPT/PBEF/Visfatin Recombinant Monoclonal Antibody [BLR058F]

    (#MBS3906306)

    Gene Names:
    NAMPT/PBEF; NAMPT; VF; PBEF; PBEF1; VISFATIN; 1110035O14Rik
    Other Names:
    pre-B cell-enhancing factor; pre-B-cell colony-enhancing factor 1; nicotinamide phosphoribosyltransferase; NAmPRTase
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human, Mouse
    Purification:
    Purified
    Applications:
    Western Blot (WB), Immunoprecipitation (IP), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Flow Cytometry (FC/FACS)
    GSTO2

    Recombinant Human GSTO2

    (#MBS7614854)

    Gene Names:
    GSTO2; GSTO 2-2; bA127L20.1
    Other Names:
    glutathione dependent dehydroascorbate reductase; Glutathione S transferase like protein; Glutathione S transferase omega 2; glutathione S transferase omega 2 2; Glutathione S-transferase omega-2; GST...
    Host/Reactivities:
    Host: E Coli
    Purity:
    Greater than 95% by SDS-PAGE gel analyses
    Applications:
    Western Blot (WB), ELISA (EIA)
    Transcobalamin II, Macrocytic Anemia (TCN2)

    Cy3-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

    (#MBS2166232)

    Gene Names:
    TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
    Other Names:
    Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
    Host/Reactivities:
    Host: Mouse / Reactivity: Human
    Purification:
    Protein A + Protein G affinity chromatography
    Applications:
    Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
    Western Blot (WB)

    Pantothenate Kinase 1, NT (Pantothenic Acid Kinase 1, PANK1, PANK1a, PANK1b, PANK, hPanK1, hPanK, MGC24596) (FITC)

    (#MBS6491891)

    Gene Names:
    PANK1; PANK
    Other Names:
    EC=2.7.1.33; pantothenate kinase 1 isoform alpha; pantothenate kinase 1
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human, Mouse
    Purification:
    Purified by Protein G Affinity Chromatography.
    Isotype/Clone:
    Isotype: IgG
    Applications:
    Western Blot (WB), FLISA
    BTD

    Human BTD Protein Lysate

    (#MBS138115)

    Gene Names:
    BTD
    Other Names:
    biotinidase; biotinidase isoform 3
    Host/Reactivities:
    Host: Human
    MRP1

    MRP1 Rabbit mAb

    (#MBS4762160)

    Gene Names:
    ABCC1; MRP1; MRP; ABCC; GS-X; ABC29
    Other Names:
    GSX; Leukotriene C(4) transporter; LTC4 transporter; Multidrug resistance-associated protein 1; ATP-binding cassette; sub-family C (CFTR/MRP); member 1
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human
    Purification:
    Affinity Chromatography
    Isotype/Clone:
    Isotype: IgG / Clone R04-2D9
    Applications:
    Western Blot (WB), Flow Cytometry (FC/FACS)
    Western Blot (WB)

    MMACHC, CT (MMACHC, Methylmalonic aciduria and homocystinuria type C protein) (Azide free) (HRP)

    (#MBS6321244)

    Gene Names:
    MMACHC; cblC
    Other Names:
    Methylmalonic aciduria and homocystinuria type C protein; methylmalonic aciduria (cobalamin deficiency) cblC type; with homocystinuria
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human
    Purification:
    Purified by Protein A Affinity Chromatography.
    Isotype/Clone:
    Isotype: IgG
    Applications:
    Western Blot (WB), ELISA (EIA)
    Western Blot (WB)

    MCCC2 (MCCB, Methylcrotonoyl-CoA Carboxylase beta Chain, Mitochondrial, 3-methylcrotonyl-CoA Carboxylase 2, 3-methylcrotonyl-CoA Carboxylase Non-biotin-containing Subunit, 3-methylcrotonyl-CoA:carbon Dioxide Ligase Subunit beta) (PE)

    (#MBS6385081)

    Gene Names:
    MCCC2; MCCB
    Other Names:
    methylcrotonoyl-CoA carboxylase beta chain; mitochondrial; methylcrotonoyl-CoA carboxylase 2 (beta)
    Host/Reactivities:
    Host: Rabbit / Reactivity: Human
    Purification:
    Purified by Protein A Affinity Chromatography.
    Isotype/Clone:
    Isotype: IgG
    Applications:
    Western Blot (WB)
    Transcobalamin II, Macrocytic Anemia (TCN2)

    HRP-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

    (#MBS2167964)

    Gene Names:
    TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
    Other Names:
    Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
    Host/Reactivities:
    Host: Mouse / Reactivity: Human
    Purification:
    Protein A + Protein G affinity chromatography
    Applications:
    Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
    Transcobalamin II, Macrocytic Anemia (TCN2)

    FITC-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

    (#MBS2143342)

    Gene Names:
    TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
    Other Names:
    Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
    Host/Reactivities:
    Host: Mouse / Reactivity: Human
    Purification:
    Protein A + Protein G affinity chromatography
    Isotype/Clone:
    Isotype: IgG / Clone C1
    Applications:
    Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
    • Western Blot (WB)
    • Immunofluorescence (IF)

      LMBRD1 Polyclonal Antibody

      (#MBS2574014)

      Gene Names:
      LMBRD1; NESI; LMBD1; MAHCF; C6orf209
      Other Names:
      probable lysosomal cobalamin transporter; LMBR1 domain containing 1
      Host/Reactivities:
      Host: Rabbit / Reactivity: Human, Mouse
      Purification:
      Affinity purification
      Isotype/Clone:
      Isotype: IgG
      Applications:
      Western Blot (WB), Immunofluorescence (IF)
      Transcobalamin II, Macrocytic Anemia (TCN2)

      Biotin-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

      (#MBS2167097)

      Gene Names:
      TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
      Other Names:
      Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
      Host/Reactivities:
      Host: Mouse / Reactivity: Human
      Purification:
      Protein A + Protein G affinity chromatography
      Applications:
      Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
      PNPO

      PNPO Antibody

      (#MBS8595151)

      Gene Names:
      PNPO; PDXPO; HEL-S-302
      Other Names:
      pyridoxine-5'-phosphate oxidase; pyridoxamine 5'-phosphate oxidase
      Host/Reactivities:
      Host: Rabbit / Reactivity: Human, Mouse, Rat
      Purification:
      Antigen affinity purification
      Isotype/Clone:
      Isotype: Rabbit IgG
      Applications:
      Immunohistochemistry (IHC)
      SDS-Page

      Recombinant Human MMAB Protein, N-His

      (#MBS1587714)

      Gene Names:
      MMAB; ATR; cob; cblB; CFAP23
      Other Names:
      Methylmalonic aciduria type B protein; Cob(II)yrinic acid a; c-diamide adenosyltransferase; Cobinamide/cobalamin adenosyltransferase; Corrinoid adenosyltransferase; Cob(II)alamin adenosyltransferase; ...
      Host/Reactivities:
      Host: E coli
      Purity:
      >90% as determined by SDS-PAGE.
      Applications:
      ELISA (EIA), Immunogen, SDS-PAGE, Western Blot (WB), Bioactivity testing in progress
      Western Blot (WB)

      Anti-SLC52A3 Antibody

      (#MBS8325495)

      Gene Names:
      SLC52A3; RFT2; BVVLS; RFVT3; hRFT2; BVVLS1; C20orf54; bA371L19.1
      Other Names:
      solute carrier family 52; riboflavin transporter; member 3; solute carrier family 52 (riboflavin transporter)
      Host/Reactivities:
      Host: Rabbit / Reactivity: Human
      Purification:
      The antibody was purified by immunogen affinity chromatography.
      Applications:
      Western Blot (WB), Flow Cytometry (FC/FACS)
      ACP5

      ACP5 (Tartrate-resistant Acid Phosphatase Type 5, TR-AP, Tartrate-resistant Acid ATPase, TrATPase, Type 5 Acid Phosphatase) (MaxLight 750)

      (#MBS6368624)

      Gene Names:
      ACP5; TRAP; SPENCDI
      Other Names:
      tartrate-resistant acid phosphatase type 5; acid phosphatase 5; tartrate resistant
      Host/Reactivities:
      Host: Rabbit / Reactivity: Human
      Purification:
      Purified by Protein A Affinity Chromatography.
      Isotype/Clone:
      Isotype: IgG
      Applications:
      Western Blot (WB)
      PPCS/Phosphopantothenate--cysteine ligase

      Human PPCS/Phosphopantothenate--cysteine ligase ELISA Kit

      (#MBS2906773)

      Gene Names:
      PPCS
      Other Names:
      Phosphopantothenoylcysteine synthetase; PPC synthetase; COAB; Phosphopantothenate--cysteine ligase; phosphopantothenate--cysteine ligase isoform b
      Host/Reactivities:
      Reactivity: Human
      Assay Type
      Sandwich
      Detection Range
      0.312-20ng/mL
      Sensitivity
      0.155ng/mL
      • Western Blot (WB)
      • Western Blot (WB)

        PDXK (Pyridoxal Kinase, Pyridoxine Kinase, C21orf97, C21orf124, DKFZp566A071, FLJ31940, FLJ37311, MGC15873, MGC31754, MGC52346, PKH, PNK, PRED79) (AP)

        (#MBS6388976)

        Gene Names:
        PDXK; PKH; PNK; PRED79; C21orf97; HEL-S-1a; C21orf124
        Other Names:
        pyridoxal kinase; pyridoxal (pyridoxine; vitamin B6) kinase
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human
        Purification:
        Purified by Protein A Affinity Chromatography.
        Isotype/Clone:
        Isotype: IgG
        Applications:
        Western Blot (WB)
        NAMPT/PBEF/Visfatin

        Rabbit anti-NAMPT/PBEF/Visfatin Recombinant Monoclonal Antibody [BLR058F]

        (#MBS3906307)

        Gene Names:
        NAMPT/PBEF; NAMPT; VF; PBEF; PBEF1; VISFATIN; 1110035O14Rik
        Other Names:
        pre-B cell-enhancing factor; pre-B-cell colony-enhancing factor 1; nicotinamide phosphoribosyltransferase; NAmPRTase
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human, Mouse
        Purification:
        Purified
        Applications:
        Western Blot (WB), Immunoprecipitation (IP), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Flow Cytometry (FC/FACS)
        NAMPT

        Research Grade Anti-Human NAMPT Antibody (Alt-100)

        (#MBS1580618)

        Gene Names:
        NAMPT; VF; PBEF; PBEF1; VISFATIN; 1110035O14Rik
        Other Names:
        Alt-100; Alt 100; Alt100; Nicotinamide phosphoribosyltransferase
        Host/Reactivities:
        Reactivity: Human
        Purification:
        >95% by SDS-PAGE.Protein A/G purified from cell culture supernatant.
        Isotype/Clone:
        Isotype: IgG
        Applications:
        Research Grade Biosimilar
        TCblR

        Recombinant Human TCblR

        (#MBS7621599)

        Gene Names:
        TCblR; CD320; 8D6; 8D6A
        Other Names:
        CD320 antigen; 8D6 antigen; FDC-signaling molecule 8D6; FDC-SM-8D6; Transcobalamin receptor; CD320 molecule
        Host/Reactivities:
        Host: Mammalian Cells
        Purity:
        Greater than 85% as determined by SDS-PAGE.
        Applications:
        Western Blot (WB), ELISA (EIA)
        Western Blot (WB)

        PNPO, CT (PNPO, Pyridoxine-5'-phosphate oxidase, Pyridoxamine-phosphate oxidase) (FITC)

        (#MBS6335436)

        Gene Names:
        PNPO; PDXPO; HEL-S-302
        Other Names:
        Pyridoxine-5'-phosphate oxidase; Pyridoxamine-phosphate oxidase; pyridoxamine 5'-phosphate oxidase
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human
        Purification:
        Purified by Protein A Affinity Chromatography.
        Isotype/Clone:
        Isotype: IgG
        Applications:
        Western Blot (WB), FLISA
        PNPO

        PNPO Antibody

        (#MBS8595152)

        Gene Names:
        PNPO; PDXPO; HEL-S-302
        Other Names:
        pyridoxine-5'-phosphate oxidase; pyridoxamine 5'-phosphate oxidase
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human
        Purification:
        Antigen affinity purification
        Isotype/Clone:
        Isotype: Rabbit IgG
        Applications:
        Western Blot (WB)
        MCCC2

        MCCC2, CT (MCCC2, MCCB, Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial, 3-methylcrotonyl-CoA carboxylase 2, 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit, 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta) (MaxLight 405)

        (#MBS6319589)

        Gene Names:
        MCCC2; MCCB
        Other Names:
        Methylcrotonoyl-CoA carboxylase beta chain; mitochondrial; 3-methylcrotonyl-CoA carboxylase 2; 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit; 3-methylcrotonyl-CoA:carbon dioxide ligas...
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human
        Purification:
        Purified by Protein A Affinity Chromatography.
        Isotype/Clone:
        Isotype: IgG
        Applications:
        Western Blot (WB), FLISA
        COASY

        COASY Rabbit Polyclonal Antibody

        (#MBS9513987)

        Gene Names:
        COASY; PSEC0106; NBP; DPCK; PPAT; UKR1; NBIA6; pOV-2
        Other Names:
        BH6842; Bifunctional coenzyme A synthase (CoA synthase)(NBP)(POV-2) [Includes: Phosphopantetheine adenylyltransferase (EC 2.7.7.3)(Dephospho-CoA pyrophosphorylase)(Pantetheine-phosphate adenylyltransf...
        Host/Reactivities:
        Host: Rabbit / Reactivity: Human, Mouse
        Purification:
        The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
        Applications:
        Western Blot (WB), ELISA (EIA)
        • Immunohistochemistry (IHC)
        • Immunoprecipitation (IP)
        • Western Blot (WB)
        • Western Blot (WB)

          Rabbit anti-PBEF Antibody, Affinity Purified

          (#MBS3900964)

          Gene Names:
          PBEF; NAMPT; VF; PBEF1; VISFATIN; 1110035O14Rik
          Other Names:
          pre-B cell-enhancing factor; pre-B-cell colony-enhancing factor 1; nicotinamide phosphoribosyltransferase; NAmPRTase
          Host/Reactivities:
          Host: Rabbit / Reactivity: Human, Mouse
          Purification:
          Antigen Affinity Purified
          Applications:
          Western Blot (WB), Immunoprecipitation (IP), Immunohistochemistry (IHC)
          NAPRT1

          NAPRT1 Polyclonal Antibody FITC Conjugated

          (#MBS9463102)

          Gene Names:
          NAPRT1; NAPRT; PP3856
          Other Names:
          nicotinate phosphoribosyltransferase isoform 1; nicotinate phosphoribosyltransferase
          Host/Reactivities:
          Host: Rabbit / Reactivity: Human, Mouse
          Purification:
          affinity purified by Protein A
          Applications:
          Immunocytochemistry (ICC), Immunofluorescence (IF)
          Transcobalamin II, Macrocytic Anemia (TCN2)

          Cy3-Linked Monoclonal Antibody to Transcobalamin II, Macrocytic Anemia (TCN2)

          (#MBS2166233)

          Gene Names:
          TCN2; II; TC; TC2; TC-2; TCII; TC II; D22S676; D22S750
          Other Names:
          Transcobalamin II; Macrocytic Anemia; transcobalamin-2 isoform 2
          Host/Reactivities:
          Host: Mouse / Reactivity: Human
          Purification:
          Protein A + Protein G affinity chromatography
          Applications:
          Western Blot (WB), Immunohistochemistry (IHC), Immunocytochemistry (ICC), Immunoprecipitation (IP)
          TCblR

          Recombinant Human TCblR

          (#MBS7621217)

          Gene Names:
          TCblR; CD320; 8D6; 8D6A
          Other Names:
          CD320 antigen; 8D6 antigen; FDC-signaling molecule 8D6; FDC-SM-8D6; Transcobalamin receptor; CD320 molecule
          Host/Reactivities:
          Host: Mammalian Cells
          Purity:
          Greater than 95% as determined by SDS-PAGE.
          Applications:
          Western Blot (WB), ELISA (EIA)
          SDS-Page

          Recombinant Human PCCB, N-His

          (#MBS1573017)

          Gene Names:
          PCCB
          Other Names:
          PCCase subunit beta; Propanoyl-CoA:carbon dioxide ligase subunit beta; Propionyl-CoA carboxylase beta chain; mitochondrial; mitochondrial isoform 1; propionyl CoA carboxylase; beta polypeptide
          Host/Reactivities:
          Host: E coli
          Purity:
          >90% as determined by SDS-PAGE
          Applications:
          SDS-PAGE (SDS), Western Blot (WB), ELISA (EIA), Immunogen

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